Nevertheless, multicentric visceral tumors are associated with high mortality.In this report, imaging findings of a case of infantile myofibromatosis with liver and both adrenal glands involvement; and another case with involvement of posterior thoracal and servical region muscles are presented.
📌 3 Key Takeaways
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Objective & Hypothesis:Infantile myofibromatosis is a rare myofibroblastic tumor in which soft tissue, bone and rarily visceral involvement can be seen.
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Key Findings & Data:It is usually a solitary tumor, however, multicentric involvement may also be present.
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Conclusion & Impact:Nevertheless, multicentric visceral tumors are associated with high mortality.In this report, imaging findings of a case of infantile myofibromatosis with liver and both adrenal glands involvement; and another case with involvement of posterior thoracal and servical region muscles are presented.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters
Abstract
Infantile myofibromatosis is a rare myofibroblastic tumor in which soft tissue, bone and rarily visceral involvement can be seen. It is usually a solitary tumor, however, multicentric involvement may also be present. The cases with solitary or multiple lesions but no visceral involvement have good prognosis and spontaneous regression can often be seen. Nevertheless, multicentric visceral tumors are associated with high mortality.In this report, imaging findings of a case of infantile myofibromatosis with liver and both adrenal glands involvement; and another case with involvement of posterior thoracal and servical region muscles are presented.
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Cite This Article
YEKELER, E., TUNACI, M., ACUNAŞ, G., DEMİR, F., KILINÇASLAN, H., TEPELER, A., DURSUN, M. (2022). Two cases of infantile myofibromatosis: Multiple visceral involvement and a solitary soft tissue mass. Göztepe Tıp Dergisi, Cilt: 20 - Sayı: 2, 120–122. https://ajindex.com/articles/526413
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