Journals / Göztepe Tıp Dergisi / 2009 / Cilt: 24 - Sayı: 2

Caroli’s disease: A case report

Caroli hastalığı: Bir olgu sunumu

Pages
92–94
Publication Date
2022-10-17
DOI
—
🏛️Bibliographic metadata and full text access for this article are provided via DergiPark.
DergiPark Record ↗
✨

AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this study, we present a case of a fifty year old grill who was diagnosid with Caroli’s disease (Caroli type I).

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Caroli’s disease is a rare congenital disorder characterized by cytic dilatation of the intrahepatic bile ducts.
📊
Key Findings & Data:Caroli’s disease is transmitted in autosomal recessive fashion.
💡
Conclusion & Impact:In this study, we present a case of a fifty year old grill who was diagnosid with Caroli’s disease (Caroli type I).
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Caroli’s disease is a rare congenital disorder characterized by cytic dilatation of the intrahepatic bile ducts. Caroli’s disease is transmitted in autosomal recessive fashion. Chollangitis, liver cirrhosis, and cholangiocarcinoma are its potantial complications. The magnetic resonance cholangiography (MRCG) is the metod with the highest sensitivity in the diagnosis of Caroli’s disease. In this study, we present a case of a fifty year old grill who was diagnosid with Caroli’s disease (Caroli type I).

Özet

Caroli hastalığı karaciğer içi safra yollarının kistik genişlemesi ile karakterize nadir konjenital bir bozukluktur. Caroli hastalığı otozomal resesif olarak geçiş gösterir. Kolanjitis, karaciğer sirozu ve kolanjiyokarsinom potansiyel komplikasyonlarıdır. Magnetik rezonans kolanjiografi (MRKG) Caroli hastalığının tanısında duyarlılığı en yüksek olan metottur. Bu çalışmada, Caroli hastalığı (caroli tip I) tanısı ile 15 yaşında bir kız çocuğunu sunduk.

🔖

Cite This Article

DORU, İ., KARAMAN, A., BİNİCİ, N. D. (2022). Caroli’s disease: A case report. Göztepe Tıp Dergisi, Cilt: 24 - Sayı: 2, 92–94. https://ajindex.com/articles/526239

📄 Full Text PDF Viewer

📄

PDF görüntüleyici hazırlanıyor...

References (18)

  1. Caroli J. Disease of the intrahepatic bile ducts. Minerva Med 1972;29:5279-5291
  2. Parada LA, Hallen M, Hagerstrand I, Tranberg KG, Johansson B. Clonal chromosomal abnormalities in congenital bile duct dilatation (Caroli’s disease). Gut 1999;45:780-782
  3. Chiba T, Shinozaki M, Kato S, Goto N, Fujimato H, Kodo F. Caroli’s disease: central dot sign re-examined by CT arteriography and CT during arterial portography. Eur Radiol 2002;12:701-702
  4. Hussain SZ, Bloom DA, Tolia V. Caroli’s disease diagnosed in a child by MRCP. Clin Imaging 2002;24:289-291
  5. Li DY, Schwarz BK. Congenital and structural abnormalities of the liver. In: Kelly AD (ed). Liver disease in children. Second edition. Oxford; Blackwell 2004:162-82
  6. Keane F, Hadzic N, Wilkinson ML, et al. Neonatal presentation of Caroli's disease. Arch Dis Child Fetal Neonatal Ed 1997;77:F145-6
  7. Levy AD, Rohrmann CA Jr, Murakata LA, et al. Caroli's disease: radiologic spectrum with pathologic correlation. AJR Am J Roentgenol 2002;179:1053-7
  8. Desmet VJ. Pathogenesis of ductal plate malformation. J Gastroenterol Hepatol 2004;19:356-60
  9. Desmet VJ. Ludwig symposium on biliary disorders-Part I. Pathogenesis of ductal plate abnormalities. Mayo Clin Proc 1998;73:80-9
  10. Giovanardi RO. Monolobar Caroli's disease in an adult. Case report. Hepatogastroenterology 2003;50:2185-7 11. Gupta AK, Gupta A, Bhardwaj VK, et al. Caroli's disease. Indian J Pediatr 2006;73:233-5
  11. Yonem O, Bayraktar Y. Clinical characteristics of Caroli's disease. World J Gastroenterol 2007;13:1930-3
  12. De Kerckhove L, De Meyer M, Verbaandert C, et al. The place of liver transplantation in Caroli's disease and syndrome. Transpl Int 2006;19:381-8
  13. Patil S, Das HS, Desai N, et al. Caroli's syndrome-a rare cause of portal hypertension. J Assoc Physicians India 2004;52:261
  14. Sharma R, Mondal A, Taneja V, et al. Radionuclide scintigraphy in Caroli's disease. Indian J Pediatr 1997;64:105-7
  15. Asselah T, Ernst O, Sergent G, et al. Caroli's disease: a magnetic resonance cholangiopancreatography diagnosis. Am J Gastroenterol 1998;93:109-10
  16. Ros E, Navarro S, Bru C, et al. Ursodeoxycholic acid treatment of primary hepatolithiasis in Caroli's syndrome. Lancet 1993;342:404-6
  17. Bockhorn M, Malago M, Lang H, et al. The role of surgery in Caroli's disease. J Am Coll Surg 2006;202:928-32
  18. Habib S, Shakil O, Couto OF, et al. Caroli's disease and orthotopic liver transplantation. Liver Transpl 2006;12:416-21.