Journals / European Journal of Rheumatology / 2015 / Cilt: 2 - Sayı: 4

Therapy resistant idiopathic scleredema: an underlying pathology not always present

Pages
163–164
Publication Date
2022-10-18
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

At present, there is no proved treatment for this disease

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Scleredema is a rare connective tissue disorder of unknown pathogenesis.
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Key Findings & Data:The patient was followed regularly for 13 years and did not respond to various combinations of immunosuppressants and psoralen plus ultraviolet A therapy.
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Conclusion & Impact:At present, there is no proved treatment for this disease
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Scleredema is a rare connective tissue disorder of unknown pathogenesis. Three types of scleredema have been described, based on its association with postinfection, monoclonal gammopathy and diabetes mellitus. We report herein a case of scleredema which the diagnosis didn't get specified. The patient was followed regularly for 13 years and did not respond to various combinations of immunosuppressants and psoralen plus ultraviolet A therapy. Treatment of scleredema is quite difficult and of limited success. At present, there is no proved treatment for this disease

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Cite This Article

ZİHNİ, F. Y., KARABULUT, G., KOÇANAOĞULLARI, H., İNAL, V., KALFA, M., EMMUNGİL, H. (2022). Therapy resistant idiopathic scleredema: an underlying pathology not always present. European Journal of Rheumatology, Cilt: 2 - Sayı: 4, 163–164. https://ajindex.com/articles/511813

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References (2)

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