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Journals / Eklem Hastalıkları ve Cerrahisi Dergisi (Eski Adı: Artroplasti Artroskopik Cerrahi Derg.) / 2016 / Cilt: 27 - Sayı: 3

Escobar (multiple pterygium) sendromu: Çok nadir bir sendroma multidisipliner yaklaşım

Escobar (multiple pterygium) syndrome: Multidisciplinary approach to a very rare syndrome

Murat Celal SÖZBİLEN
Hüseyin GÜNAY
Funda ATAMAZ ÇALIŞ
Pages
171–174
Publication Date
2022-10-18
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

As a result of the operations and physical therapy, adequate muscle strength was obtained

📌 3 Key Takeaways

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Objective & Hypothesis:Escobar (multiple pterygium) syndrome is progressive and a very rare syndrome.
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Key Findings & Data:In this report, we present the treatment management of a 14-year-old case with late stage Escobar syndrome who was admitted due to multiple pterygia and bilateral knee contractures.
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Conclusion & Impact:As a result of the operations and physical therapy, adequate muscle strength was obtained
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Escobar (multiple pterygium) syndrome is progressive and a very rare syndrome. It is generally characterized by multiple pterygia that are found in the cervical, antecubital and popliteal regions. In this report, we present the treatment management of a 14-year-old case with late stage Escobar syndrome who was admitted due to multiple pterygia and bilateral knee contractures. The treatment of this case was conducted in collaboration with the department of orthopedics and the department of physical therapy. The treatment of the case was done in three stages: soft tissue procedures, femoral recurvatum osteotomy and triple arthrodesis, respectively. In addition to all these, the patient did intensive physical therapy for one year. As a result of the operations and physical therapy, adequate muscle strength was obtained

Özet

Escobar (multiple pterygium) sendromu progresif ve oldukça nadir görülen bir sendromdur. Genellikle servikal, antekübital ve popliteal bölgede multiple pterygiumlar ile karakterize edilir. Bu yazıda, 14 yaşında multiple pterygium ve iki taraflı diz kontraktürleri olan Escobar sendromlu geç dönem bir olgunun tedavi yönetimi sunuldu. Bu olgunun tedavisi Ortopedi Anabilim Dalı ve Fizik Tedavi Anabilim Dalı bölümlerinin işbirliği ile yürütüldü. Hastanın tedavisi sırasıyla, yumuşak doku işlemi, femoral rekurvatum osteotomisi ve üçlü artrodez olmak üzere üç aşamada yapıldı. Tüm bunlara ek olarak, bir yıl boyunca yoğun fizik tedavi uygulandı. Uygulanan ameliyatlar ve fizik tedavi sonucunda, yeterli kas gücü sağlandı

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Cite This Article

SÖZBİLEN, M. C., GÜNAY, H., ÇALIŞ, F. A. (2022). Escobar (multiple pterygium) sendromu: Çok nadir bir sendroma multidisipliner yaklaşım. Eklem Hastalıkları ve Cerrahisi Dergisi (Eski Adı: Artroplasti Artroskopik Cerrahi Derg.), Cilt: 27 - Sayı: 3, 171–174. https://ajindex.com/articles/498501

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