Journals / Eastern Journal of Medicine / 2016 / Cilt: 21 - Sayı: 1

Anesthesia management of Jansen's metaphyseal dysplasia

Pages
52–53
Publication Date
2022-10-18
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this article we intended to draw attention to some issues releated with anesthesia hereby that a 9 year-old patient with Jansen's metaphyseal dysplasia.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Metaphyseal chondrodysplasia is a rare autosomal dominant disorder characterized by accumulation of cartilage in specifically metaphysis of tubular bones.
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Key Findings & Data:Hyperkalemia and hypophosphatemia were seen most of these patients.
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Conclusion & Impact:In this article we intended to draw attention to some issues releated with anesthesia hereby that a 9 year-old patient with Jansen's metaphyseal dysplasia.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Metaphyseal chondrodysplasia is a rare autosomal dominant disorder characterized by accumulation of cartilage in specifically metaphysis of tubular bones. Hyperkalemia and hypophosphatemia were seen most of these patients. In this article we intended to draw attention to some issues releated with anesthesia hereby that a 9 year-old patient with Jansen's metaphyseal dysplasia.

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Cite This Article

GOKTAS1, U. (2022). Anesthesia management of Jansen's metaphyseal dysplasia. Eastern Journal of Medicine, Cilt: 21 - Sayı: 1, 52–53. https://ajindex.com/articles/494864

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References (6)

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  2. Jansen M. 1934 Übber atypische Chondrodystrophie (Achondroplasie) und über eine noch nicht beschriebene angeborene Wachstumsstarung des Knochensystems: Metaphysare Dysostosis. Z Orthop Chir 1934; 61: 253-286
  3. Gordon SL, Varano LA, Alandete A, Maisels MJ. Jansen's metaphyseal dysostosis. Pediatrics 1976; 58: 556-560
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  5. Kikuchi S, Hasue M, Watanabe M, Hasebe K. Metaphysial Dysostosis (Jansen Type). The Journal of Bone and Joınt Surgery 1976; 58: 102-106
  6. Kruse K, Schutz C. Calcium metabolism in the Jansen type of metaphyseal dysplasia. Eur J Pediatr 1993; 152: 912-915.