We discuss the diagnosis, treatment and the differential diagnosis of paranasal sinus involvement in Wegener s granulomatosis in the light of literature data.
📌 3 Key Takeaways
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Objective & Hypothesis:Wegener s granulomatosis which is rarely seen in children is an idiopathic necrotizing granulomatous vasculitis, affecting primarily paranasal sinuses, nasopharynx, lungs, kidneys and joints.
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Key Findings & Data:In this article, we report a very rare case of eight-year-old boy presenting with Wegener s granulomatosis of paranasal sinuses without lung, kidney and any other organ involvement.
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Conclusion & Impact:We discuss the diagnosis, treatment and the differential diagnosis of paranasal sinus involvement in Wegener s granulomatosis in the light of literature data.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters
Abstract
Wegener s granulomatosis which is rarely seen in children is an idiopathic necrotizing granulomatous vasculitis, affecting primarily paranasal sinuses, nasopharynx, lungs, kidneys and joints. In this article, we report a very rare case of eight-year-old boy presenting with Wegener s granulomatosis of paranasal sinuses without lung, kidney and any other organ involvement. We discuss the diagnosis, treatment and the differential diagnosis of paranasal sinus involvement in Wegener s granulomatosis in the light of literature data.
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Cite This Article
TOPALOĞLU, R., DURSUN, İ., DAAR, G., KARA, A., CENGİZ, A. B., YÜCEL, Ö. T. (2022). Wegener's granulomatosis presenting with an ısolated paranasal sinus ınvolvement in a child. Archives of Rheumatology, Cilt: 29 - Sayı: 2, 130–133. https://ajindex.com/articles/448060
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