SavedAdd your journal

Journals / Türk Göğüs Kalp Damar Cerrahisi Dergisi / 2002 / Cilt: 10 - Sayı: 2

Mounier-Kuhn syndrome: Case report

Mounier-Kuhn sendromu: Olgu sunumu

Alpay SARPER
Necdet ÖZ
Abid DEMİRCAN
Erol IŞIN
Pages
116–117
Publication Date
2022-09-02
DOI
—
🏛️Bibliographic metadata and full text access for this article are provided via DergiPark.
DergiPark Record ↗
✨

AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

The patent is asymptomatic during four-year follow-up.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Mounier - Kuhn syndrome is a rare congenital disorder due to defective development of elastic and muscle tissues in the upper airways.
📊
Key Findings & Data:A case presented with a severe life threatening pneumonia, bilateral bronchiectasia and tracheobronkomegaly.
💡
Conclusion & Impact:The patent is asymptomatic during four-year follow-up.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Mounier - Kuhn syndrome is a rare congenital disorder due to defective development of elastic and muscle tissues in the upper airways. A case presented with a severe life threatening pneumonia, bilateral bronchiectasia and tracheobronkomegaly. Right pneumonectomy was performed. Symptom of the infection was diminished after the operation. The patent is asymptomatic during four-year follow-up.

Özet

Mounier - Kuhn sendromu nadir görülen, üst solunum yolunda elastik ve musküler dokudaki defekt sonucu oluşan, konjenital bir hastalıktır. Sunduğumuz olgu hemoptizi, tekrarlayan ağır pnömoni atakları ve tek taraflı kistik bronşektazi ile birlikte seyreden trakeobronkomegali olgusudur. Hastaya sağ pnömonektomi uygulanmıştır. Operasyondan sonra belirgin klinik düzelme görüldü ve hasta halen 4 yıldır kontrol altında sağlıklı olarak hayatına devam etmektedir.

🔖

Cite This Article

SARPER, A., ÖZ, N., DEMİRCAN, A., IŞIN, E. (2022). Mounier-Kuhn syndrome: Case report. Türk Göğüs Kalp Damar Cerrahisi Dergisi, Cilt: 10 - Sayı: 2, 116–117. https://ajindex.com/articles/425465

📄 Full Text PDF Viewer

📄

PDF görüntüleyici hazırlanıyor...

References (6)

  1. Hering T, Rossdeutscher R, Kaiser D. Mounier-Kuhn disease / Tracheobronc home galy. Pneumologi 1990;44:507-8
  2. Morton NS. Bronchiectasis. In: Fischman A P, ed. Pulmonary Diseases and Disorders. New York: Mc Graw & Hill Book, 1988:1553-81
  3. Woodring JH, Howard RS, Rehm SR. Congenital tracheobronchomegaly (Mounier - Kuhn syndrome): A report of 10 cases and review of the literature. J Thorac Imaging 1991;6:1-10
  4. Benesch M, Eber E, Pfleger A, Zach MS. Recurrent lower respiratory tract infections in a 14-year-old boy with tracheobronchomegaly (Mounier-Kuhn syndrome). Pediatr Pulmonol 2000;29:476-9
  5. Yılmaz A, Coşkunsel M, Işık R. Mounier-Kuhn sendromu. Solunum Hastalıkları Derg 1991;2:283-6
  6. Beachlcy MC, Ghahremani GG. Tracheobronchomegaly (Mounier - Kuhn syndrome) South Med J 1976;69:1228-9.