Norwood stage 1 operation with sano modification

Key Findings & Data:This syndrome is characterized by hypoplasia or absence of the left ventricle, mitral and aortic valve, and severe hypoplasia of the ascending aorta.

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Conclusion & Impact:This case report presents a successful Norwood stage 1 palliation with Sano modification in a patient with HLHS diagnosed in fetal period.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Domain Parameters

Abstract

Hypoplastic left heart syndrome (HLHS) is a very unique ‘single ventricle pathology’ among congenital cardiac anomalies. This syndrome is characterized by hypoplasia or absence of the left ventricle, mitral and aortic valve, and severe hypoplasia of the ascending aorta. While an aortopulmonary shunt is used for pulmonary circulation in classical Norwood procedure which is a first stage palliation, right ventricle to pulmonary artery shunt is used in Sano modification. This case report presents a successful Norwood stage 1 palliation with Sano modification in a patient with HLHS diagnosed in fetal period.

Özet

Hipoplastik sol kalp sendromu (HSKS) doğuştan kalp anomalileri içinde özel bir yeri olan ‘tek ventrikül patolojisi’dir. Bu patoloji; sol ventrikül, mitral kapak ve aort kapağı hipoplazisi veya yokluğu ve çıkan aortanın ağır hipoplazisi ile karakterizedir. İlk aşama palyasyonunda uygulanan klasik Norwood ameliyatında şant, pulmoner arter ile sistemik arter arasına uygulanırken, Sano modifikasyonunda şant, sağ ventrikül ile pulmoner arter arasına yerleştirilmektedir. Bu yazıda fötal dönemde tespit edilen HSKS’li olguya başarılı bir şekilde uygulanan Sano yöntemi ile modifiye edilmiş ilk aşama Norwood palyatif ameliyatı sunuldu.

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Cite This Article

ÖZYÜREK, A. R., DEĞİRMENCİLER, K., ARPAÇAY, A., ATAY, Y., ALAYUNT, E. A., AŞKAR, F. Z. (2022). Norwood stage 1 operation with sano modification. Türk Göğüs Kalp Damar Cerrahisi Dergisi, Cilt: 16 - Sayı: 2, 122–125. https://ajindex.com/articles/425081

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