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Journals / Türk Göğüs Kalp Damar Cerrahisi Dergisi / 2014 / Cilt: 22 - Sayı: 4

Mitral regurgitation in a patient with Noonan syndrome: re-do mitral valve repair via mini-thoracotomy

Noonan sendromlu bir hastada mitral yetmezlik: mini-torakotomi ile mitral kapağın yeniden tamiri

Pil Je KANG
Hyung Gon JE
Sang Kwon LEE
Pages
821–825
Publication Date
2022-09-02
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

This minimally invasive approach may be an optimal alternative for early recovery in patients with these characteristics.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:In this article, we present a 38-year-old male case with Noonan syndrome who underwent repair for an atrial septal defect (ASD) at the age of 14.
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Key Findings & Data:Severe mitral regurgitation, mild tricuspid regurgitation, and residual ASD were detected on echocardiography.
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Conclusion & Impact:This minimally invasive approach may be an optimal alternative for early recovery in patients with these characteristics.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

In this article, we present a 38-year-old male case with Noonan syndrome who underwent repair for an atrial septal defect (ASD) at the age of 14. Severe mitral regurgitation, mild tricuspid regurgitation, and residual ASD were detected on echocardiography. As repeated sternotomy was hindered by a severely dilated cardiac chamber with retrosternal adhesion and a suprasternally located aortic arch, we performed a right anterolateral thoracotomy approach with peripheral cannulation. This minimally invasive approach may be an optimal alternative for early recovery in patients with these characteristics.

Özet

Bu yazıda, 14 yaşında atriyal septal defekt (ASD) tamiri yapılan Noonan sendromlu 38 yaşında bir erkek olgu sunuldu. Ekokardiyografide şiddetli mitral yetmezlik, hafif triküspid yetmezlik ve rezidüel ASD tespit edil- di. Retrosternal adezyona bağlı şiddetli düzeyde dilate olmuş kalp odacığı ve suprasternal yerleşimli aort arkının sternotomi tekrarına engel olması nedeniyle, periferik kanülasyon ile sağ anterolateral torakotomi yaklaşımı uygulandı. Bu minimal invaziv yaklaşım, bu özelliklere sahip hastalarda erken iyileşme için iyi bir alternatif olabilir.

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Cite This Article

KANG, P. J., JE, H. G., LEE, S. K. (2022). Mitral regurgitation in a patient with Noonan syndrome: re-do mitral valve repair via mini-thoracotomy. Türk Göğüs Kalp Damar Cerrahisi Dergisi, Cilt: 22 - Sayı: 4, 821–825. https://ajindex.com/articles/424329

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References (6)

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