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Journals / Türk Göğüs Kalp Damar Cerrahisi Dergisi / 2020 / Cilt: 28 - Sayı: 1

Pleuropulmonary blastoma: A report of two cases

Plöropulmoner blastom: İki olgu sunumu

Ömer Faruk DEMİR
Ömer ÖNAL
Leyla HASDIRAZ
Fahri OĞUZKAYA
Ayşe ÜLGEY
Olgun KONTAŞ
Pages
209–212
Publication Date
2022-09-02
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Herein, we present two cases of pleuropulmonaryblastoma type 3 presenting with pneumothorax, a rare clinicalpresentation of pleuropulmonary blastoma, which wassuccessfully treated with surgery.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Pleuropulmonary blastoma is a rare and aggressive childhoodtumor of mesenchymal origin.
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Key Findings & Data:It has a poor prognosis andmainly classified as cystic (type 1), mixed type (type 2), andsolid (type 3).
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Conclusion & Impact:Herein, we present two cases of pleuropulmonaryblastoma type 3 presenting with pneumothorax, a rare clinicalpresentation of pleuropulmonary blastoma, which wassuccessfully treated with surgery.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Pleuropulmonary blastoma is a rare and aggressive childhoodtumor of mesenchymal origin. It has a poor prognosis andmainly classified as cystic (type 1), mixed type (type 2), andsolid (type 3). Herein, we present two cases of pleuropulmonaryblastoma type 3 presenting with pneumothorax, a rare clinicalpresentation of pleuropulmonary blastoma, which wassuccessfully treated with surgery.

Özet

Plöropulmoner blastom çocukluk çağında mezenkimal kökenli, nadir ve agresif bir tümördür. Prognozu kötü olup, başlıca kistik (tip 1), mikst tip (tip 2) ve solid (tip 3) olarak sınıflandırılır. Bu yazıda plöropulmoner blastomun nadir bir klinik tablosu olan pnömotoraksın eşlik ettiği ve cerrahi ile başarılı bir şekilde tedavi edilen iki plöropulmoner blastom tip 3 olgusu sunuldu.

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Cite This Article

DEMİR, Ö. F., ÖNAL, Ö., HASDIRAZ, L., OĞUZKAYA, F., ÜLGEY, A., KONTAŞ, O. (2022). Pleuropulmonary blastoma: A report of two cases. Türk Göğüs Kalp Damar Cerrahisi Dergisi, Cilt: 28 - Sayı: 1, 209–212. https://ajindex.com/articles/423676

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References (8)

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