Juvenil Pityriasis Rubra Pilaris: A Case Report

Objective & Hypothesis:Juvenile pityriasis rubra pilaris (PRP) is an uncommon skin disease characterized by follicularkeratotic papules, erythemato-squamous plaques and palmoplantar keratoderma.

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Key Findings & Data:A 8 years-old boy presented with a 15 days history of scaly patches and plaques withfollicular papules involving his scalp and face.

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Conclusion & Impact:We presented our case because of its rarity

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Jüvenil pitriyazis rubra pilaris · Juvenil pityriasis rubra pilaris

Abstract

Juvenile pityriasis rubra pilaris (PRP) is an uncommon skin disease characterized by follicularkeratotic papules, erythemato-squamous plaques and palmoplantar keratoderma. Etyology isunknown. A 8 years-old boy presented with a 15 days history of scaly patches and plaques withfollicular papules involving his scalp and face. However he had palmoplantar keratoderma onhis hands and feet. Based upon clinical and histopatological findings, he was diagnosed asJuvenile PRP. Acitretin was initiated for therapy. We presented our case because of its rarity

Özet

Jüvenil pitriyazis rubra pilaris (PRP) folliküler keratotik papüller, eritema-skuamöz plaklar vepalmoplantar keratoderma ile karakterize seyrek görülen bir deri hastalığıdır. Etiyolojisibilinmemektedir. 8 yaşındaki erkek hastanın saçlı deri ve yüzde folliküler papüllerle pullu yamave plaklar içeren 15 günlük bir öyküsü mevcuttu. Ayrıca el ve ayaklarında palmoplantarkeratoderması vardı. Klinik ve histopatolojik bulgulara dayanarak Jüvenil PRP tanısı konuldu.Tedavi için asitretin başlandı. Nadir görülen bir hastalık olduğu için bu olgumuzu sunduk

Keywords

Jüvenil pitriyazis rubra pilaris Juvenil pityriasis rubra pilaris

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Cite This Article

ALBAYRAK, H., YANIK, M. E., GÜVENÇ, S. C., ŞAHİN, A. F., GÜRLEVİK, Z. (2010). Juvenil Pityriasis Rubra Pilaris: A Case Report. Düzce Tıp Fakültesi Dergisi, Cilt: 12 - Sayı: 1, 91–93. https://ajindex.com/articles/420444

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