Marfan sendromunda Hodgkin dışı lenfoma ve aort anevrizması

Key Findings & Data:This report describes a case of Marfan syndrome who presented with chest discomfort and was diagnosed to have an aortic aneurysm and an additional incidental mediastinal mass that on further investigation turned out to be a diffuse large B cell lymphoma.

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Conclusion & Impact:We have suggested a hypothesis which can explain the occurrence of lymphoma in Marfan syndrome.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Lenfom · Hodgkin dışı · Marfan sendromu

Abstract

The combination of Marfan syndrome with lymphoma is extremely rare. This report describes a case of Marfan syndrome who presented with chest discomfort and was diagnosed to have an aortic aneurysm and an additional incidental mediastinal mass that on further investigation turned out to be a diffuse large B cell lymphoma. We have suggested a hypothesis which can explain the occurrence of lymphoma in Marfan syndrome.

Özet

Marfan sendromu ile lenfoma kombinasyonu oldukça enderdir. Bu rapor, göğüs rahatsızlığı ile gelen ve aort anevrizması ve tesadüfen ilave bir mediastinal kitlesi olduğu tespit edilen bir Marfan sendromu olgusunu anlatmaktadır. Daha ileri bir tetkik ile bu mediastinal kitlenin diffüz büyük B hücreli lenfoma olduğu açığa çıkmıştır. Marfan sendromunda lenfoma oluşumunu açıklayabilen bir hipotez ileri sürdük.

Keywords

Lenfom Hodgkin dışı Marfan sendromu Erkek Pozitron-emisyon tomografisi Yaşlı Aort anevrizması Lymphoma Non-Hodgkin Marfan Syndrome Male Positron-Emission Tomography Aged Aortic Aneurysm

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Cite This Article

GROSH, S., GROSH, S., GROSH, S. K. (2009). Marfan sendromunda Hodgkin dışı lenfoma ve aort anevrizması. Turkish Journal of Hematology, Cilt: 26 - Sayı: 1, 31–33. https://ajindex.com/articles/413180

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