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Journals / Turkish Journal of Pediatrics / 2016 / Cilt: 58 - Sayı: 4

Multisystem langerhans cell histiocytosis with thymic involvement diagnosed with anterior mediastinal mass in a 2-month-old boy

Funda TEKKEŞİN
Arzu OKUR
Betül Emine DERİNKUYU
Nalan AKYÜREK
Aynur OĞUZ
Ceyda KARADENİZ
FARUK GÜÇLÜ PINARLI
Pages
424–428
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

LCH should also be kept in mind in the differential diagnosis of skin lesions in infants, even if spontaneous regression occurs.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Tekkeşin F, Okur A, Derinkuyu BE, Akyürek N, Oğuz A, Karadeniz C, Pınarlı FG.
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Key Findings & Data:Multisystem langerhans cell histiocytosis with thymic involvement diagnosed with anterior mediastinal mass in a 2 month-old boy.
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Conclusion & Impact:LCH should also be kept in mind in the differential diagnosis of skin lesions in infants, even if spontaneous regression occurs.
🔬Design:Research Article
📍Scope:2016 Verileri
⚙️Variables:Domain Parameters

Özet

Tekkeşin F, Okur A, Derinkuyu BE, Akyürek N, Oğuz A, Karadeniz C, Pınarlı FG. Multisystem langerhans cell histiocytosis with thymic involvement diagnosed with anterior mediastinal mass in a 2 month-old boy. Turk J Pediatr 2016; 58: 424-428.Thymus gland involvement in Langerhans cell histiocytosis (LCH) is usually part of multi-system disease and may be more common than previously recognized. However, thymic involvement causing an anterior mediastinal mass is an extremely rare presentation of multisystem LCH. Here we report a 2-month-old-boy admitted to hospital with a giant anterior mediastinal mass with multisystem LCH involving the thymus, lungs, liver and skin. The differential diagnosis of mediastinal mass in children should also include LCH, especially multisystem disease. LCH should also be kept in mind in the differential diagnosis of skin lesions in infants, even if spontaneous regression occurs.

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Cite This Article

TEKKEŞİN, F., OKUR, A., DERİNKUYU, B. E., AKYÜREK, N., OĞUZ, A., KARADENİZ, C., PINARLI, F. G. (2016). Multisystem langerhans cell histiocytosis with thymic involvement diagnosed with anterior mediastinal mass in a 2-month-old boy. Turkish Journal of Pediatrics, Cilt: 58 - Sayı: 4, 424–428. https://ajindex.com/articles/412240

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