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Journals / Turkish Journal of Gastroenterology / 2010 / Cilt: 21 - Sayı: 1

Primer biliyer siroz ve akciğer tutulumu ile seyreden primer Sjögren sendromunda başarılı tedavi

Successful treatment of primary Sjögren's syndrome complicated with primary biliary cirrhosis and lung involvement

Arif ALTUNBAŞ
Güneş ARIK
Umut KALYONCI
Ali AKDOĞAN
Ömer KARADAĞ
Bünyamin KISACIK
A. İhsan ERTENLİ
Pages
60–62
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

This is the first case of Sjögren's syndrome, primary biliary cirrhosis and lymphocytic interstitial pneumonia in the English literature.

📌 3 Key Takeaways

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Objective & Hypothesis:A patient with primary Sjögren's syndrome complicated with primary biliary cirrhosis and lymphocytic interstitial pneumonia is presented.
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Key Findings & Data:She was 38 years old and was admitted to our hospital for generalized pruritus, xerostomia, xerophthalmia, fatigue, and reticulonodular changes on her chest X-ray.
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Conclusion & Impact:This is the first case of Sjögren's syndrome, primary biliary cirrhosis and lymphocytic interstitial pneumonia in the English literature.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Tomografi · Karaciğer sirozu · safra

Abstract

A patient with primary Sjögren's syndrome complicated with primary biliary cirrhosis and lymphocytic interstitial pneumonia is presented. She was 38 years old and was admitted to our hospital for generalized pruritus, xerostomia, xerophthalmia, fatigue, and reticulonodular changes on her chest X-ray. With the findings of ground-glass attenuation and centrilobular nodules in high resolution computerized tomography, the diagnosis of lymphocytic interstitial pneumonia was made. Oral methylprednisolone 1 mg/kg/day and ursodeoxycholic acid 15 mg/kg/day were started. At the 6th month follow-up, she had no complaints, and pulmonary function tests and high resolution computerized tomography were normal. This is the first case of Sjögren's syndrome, primary biliary cirrhosis and lymphocytic interstitial pneumonia in the English literature.

Özet

38 yaşında kadın, hastaneye jeneralize kaşıntı, kserostoma, kseroftalmi, halsizlik şikayetleri ile başvurdu. Arka-ön akciğer grafisinde retikülonodüler değişiklikler, yüksek çözünürlüklü akciğer tomografisinde buzlu cam dansitesi ve sentrilobüler nodüller tespit edilmesi üzerine primer biliyer siroz ve lenfositik interstisiyel pnömoni tanısı ile oral 1 mg/kg/gün metilprednizolon ve 15 mg/kg/gün dozunda ursodeoksikolik asit başlandı. Hastanın altıncı ay kontrolünde hiç bir şikayetinin kalmadığı, solunum fonksiyon testlerinin normal olduğu, yüksek çözünürlüklü akciğer tomografisindeki değişikliklerin tamamen düzeldiği saptandı. Primer biliyer siroz, lenfositik interstisiyel pnömoni ve primer Sjögren sendromu birlikteliği daha önce tanımlanmamıştır.

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Cite This Article

ALTUNBAŞ, A., ARIK, G., KALYONCI, U., AKDOĞAN, A., KARADAĞ, Ö., KISACIK, B., ERTENLİ, A. İ. (2010). Primer biliyer siroz ve akciğer tutulumu ile seyreden primer Sjögren sendromunda başarılı tedavi. Turkish Journal of Gastroenterology, Cilt: 21 - Sayı: 1, 60–62. https://ajindex.com/articles/409813

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