Journals / Turkish journal of nephrology (Online) / 2019 / Cilt: 28 - Sayı: 4

Light Chain Deposition Disease Diagnosed with Renal Biopsy: A Case Report

Pages
331–334
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

We herein present a caseof nodular glomerulosclerosis with nephrotic syndrome—a case of a 53-year-old woman who presented with acute renalfailure with no previously known disease and was diagnosed with rarely seen LCDD, and whose subsequent examinationsrevealed a plasma cell neoplasm.

📌 3 Key Takeaways

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Objective & Hypothesis:Light chain deposition disease (LCDD) is a rare disease and the most common subtype of monoclonal immunglobulindeposition disease (MCDD).
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Key Findings & Data:The most commonly affected organ is the kidney, characterized by nodular glomerulosclerosisand proteinuria at the nephrotic level.
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Conclusion & Impact:We herein present a caseof nodular glomerulosclerosis with nephrotic syndrome—a case of a 53-year-old woman who presented with acute renalfailure with no previously known disease and was diagnosed with rarely seen LCDD, and whose subsequent examinationsrevealed a plasma cell neoplasm.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Özet

Light chain deposition disease (LCDD) is a rare disease and the most common subtype of monoclonal immunglobulindeposition disease (MCDD). The most commonly affected organ is the kidney, characterized by nodular glomerulosclerosisand proteinuria at the nephrotic level. The LCDD is often associated with underlying plasma cell dyscrasias or lymphoproliferative diseases. The investigation of the underlying disease is very important for the treatment. We herein present a caseof nodular glomerulosclerosis with nephrotic syndrome—a case of a 53-year-old woman who presented with acute renalfailure with no previously known disease and was diagnosed with rarely seen LCDD, and whose subsequent examinationsrevealed a plasma cell neoplasm.

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Cite This Article

ERGEN, P., KARABULUT, Y. Y., KIYKIM, A. A., BALLI, E., KÖSE, E. Ç. (2019). Light Chain Deposition Disease Diagnosed with Renal Biopsy: A Case Report. Turkish journal of nephrology (Online), Cilt: 28 - Sayı: 4, 331–334. https://ajindex.com/articles/374863

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References (1)

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