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Journals / Zeynep Kamil Tıp Bülteni / 2009 / Cilt: 40 - Sayı: 2

A boy with thinning of flomerular basement membrane- case report

Glomeruler bazal membranda incelmesi olan bir erkek çoculc - olgu sunumu

EMRAH CAN
Seyhun SOLAKOĞLU
Ahmet NAYIR
Pages
93–96
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this article a 13 year-old boy with recurrent macroscopic haematuria, whose renal biopsy revealed thinning of glomerular basement membrane, was discussed.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Thin glomerular basement membrane disease and Alport syndrome are two hereditary nephropathies responsible for recurrent macroscopic haematuria in children.
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Key Findings & Data:Diagnosis of the both diseases usually depends on careful examination of both the clinical features of the patient and those of the family members, and evaluation of the basal membrane via electron microscopy.
💡
Conclusion & Impact:In this article a 13 year-old boy with recurrent macroscopic haematuria, whose renal biopsy revealed thinning of glomerular basement membrane, was discussed.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Ergen · Erkek · Nefrit

Abstract

Thin glomerular basement membrane disease and Alport syndrome are two hereditary nephropathies responsible for recurrent macroscopic haematuria in children. Diagnosis of the both diseases usually depends on careful examination of both the clinical features of the patient and those of the family members, and evaluation of the basal membrane via electron microscopy. In this article a 13 year-old boy with recurrent macroscopic haematuria, whose renal biopsy revealed thinning of glomerular basement membrane, was discussed.

Özet

İnce glomerüler bazal membran hastalığı(IGBMH) ve Alport sendromu(AS), çocukların tekrarlayan hematürilerinin araştırılmasında düşünülmesi gereken herediter nefropatilerdendir. Her ikisinde de hastalığın tanısı, klinik belirtilerin yanı sıra aile üyelerinin çok dikkatli incelenmesine ve bazal membran yapısının elektron mikroskop ile değerlendirilmesine dayanır. Bu yazıda tekrarlayan makroskopik hematüri nedeni ile tetkik edilen 13 yaşındaki bir erkek çocukta, elektron mikroskopisinÜe saptanan glomerüler membranda incelme bulgusu tartışılacaktır.

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Cite This Article

CAN, E., SOLAKOĞLU, S., NAYIR, A. (2009). A boy with thinning of flomerular basement membrane- case report. Zeynep Kamil Tıp Bülteni, Cilt: 40 - Sayı: 2, 93–96. https://ajindex.com/articles/335581

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References (1)

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