Pulmonary Artery Agenesis: A Case Series

Objective & Hypothesis:Pulmonary artery agenesis is a rare congenital abnormality in which atresia was encountered in the short segment of the right or left pulmonary arteries.

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Key Findings & Data:The majority of cases are diagnosed in childhood whereas some cases yield no symptoms until adulthood.

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Conclusion & Impact:We evaluated retrospectively 5 pulmonary artery agenesis cases diagnosed in our clinics between 1998-2010 with respect to the literature

🔬Design:Research Article

📍Scope:2010 Verileri

⚙️Variables:Domain Parameters

Abstract

Pulmonary artery agenesis is a rare congenital abnormality in which atresia was encountered in the short segment of the right or left pulmonary arteries. It can be isolated or associated with cardiac abnormalities such as tetralogy of Fallot, septal defects or pulmonary stenosis. The majority of cases are diagnosed in childhood whereas some cases yield no symptoms until adulthood. We evaluated retrospectively 5 pulmonary artery agenesis cases diagnosed in our clinics between 1998-2010 with respect to the literature

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Cite This Article

AĞCA, M., BULUM, S., GÜNEN, H., TOKGÖZ, F., YARKIN, T., DEMİR, M. (2015). Pulmonary Artery Agenesis: A Case Series. Solunum, Cilt: 17 - Sayı: 1, 62–66. https://ajindex.com/articles/314290

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