Journals / Medical Network Klinik Bilimler ve Doktor / 2004 / Cilt: 10 - Sayı: 2

A case of Prune-Belly syndrome diagnosed at prenatal period

Prenatal tanı konulmuş Prune-Belly sendromu olgusu

Pages
190–193
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Prune-Belly syndrome was reviewed with related literature and an usual case diagnosed at fetal ultrasonographic examination was presented.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Prune-Belly syndrome is characterized by deficient abdominal wall muscles, bilateral cryporchidism, and urinary tract abnormalities.
📊
Key Findings & Data:A fetus was diagnosed with Prune-Belly syndrome by routine ultrasonographic examination at 29th gestational week.
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Conclusion & Impact:Prune-Belly syndrome was reviewed with related literature and an usual case diagnosed at fetal ultrasonographic examination was presented.
🔬Design:Review & Systematic Survey
📍Scope:Comprehensive Sample
⚙️Variables:Doğum öncesi tanı · Prune Belly sendromu · Ultrasonografi

Abstract

Prune-Belly syndrome is characterized by deficient abdominal wall muscles, bilateral cryporchidism, and urinary tract abnormalities. A fetus was diagnosed with Prune-Belly syndrome by routine ultrasonographic examination at 29th gestational week. Although various degrees of renal involvement occur in Prune-Belly syndrome, renal dysplasia is the major determinant of fetal survival and postnatal prognosis. Prune-Belly syndrome was reviewed with related literature and an usual case diagnosed at fetal ultrasonographic examination was presented.

Özet

Prune-Belly sendromu karın kaslarının yokluğu, bilateral inmemiş testis ve üriner sistem anomalileri ile karakterize bir sendromdur. İntrauterin dönemde 29 haftalık bir fetusta rutin ultrasonografik inceleme sırasında Prune-Belly sendromu düşünüldü. Prune-Belly sendromunda çeşitli derecede renal tutulum olsa da, fetal ve postnatal prognozu belirlemede major faktör renal displazidir. Doğumdan sonra tanısı kesinleştirilen olgu literatür bilgileri eşliğinde sunuldu.

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Cite This Article

DOĞAN, Y., KILIÇ, M., TAŞKIN, E., KUMRU, S., ŞEN, Y., AYGÜN, A. D. (2004). A case of Prune-Belly syndrome diagnosed at prenatal period. Medical Network Klinik Bilimler ve Doktor, Cilt: 10 - Sayı: 2, 190–193. https://ajindex.com/articles/279114

References (16)

  1. Karakuş E.'Eldeklioğlu S, Sarı B, Hasanoğlu A. Prune-Belly sendromu (triad seridromu). Kayseri Üniversitesi Gevher Nesibe Tıp Fakültesi Mecmuası. 1982; 4:173-7.
  2. Kayacı AG, Özkan B, faşdemir HA, Şahin S. Prune-Belly sendromu: Bir vaka takdimi. Çocuk Sağlığı ve Hastalıkları Dergisi. 1993; 36:279-88.
  3. Aaberg RA, Kolye MA, Anand SK. Developmental abnormalites of the loqer urinary tract. In: Taeusch HW, Ballard RA, Awery ME, (eds). Diseases of the Newborn. Sixth Ed. Philadelphia. WB Saunders Co. 1991:880-3. Elder JS. Urologic Disorders in infants and Children.In: Behrman RE, Kliegman RM, Nelson WE. (eds). Textbook of Pediatrics. 16. Ed. Philadelphia. WB Saunders Co. 2000:1635-6.
  4. Gökalp A, Gültekin EY. Megalourethra associated with Prune-Belly sendrome. Turk J Pediatr 1993; 35:151-3.
  5. Manivel JC, Pettinato G, Reinberg Y, Gonzalez R, Burke B. Prune-Belly Syndrome: Clinicopathologic Study of 29 cases. Pediatric Pathology: 1989; 9:691-711.
  6. Terada S, Suziki N, Uchida K, Ueno H, Akasofu K. Etiology of prune-belly syndrome: evidence of megalocystic origin in an early fetus. Obstet Gynecol 1994; 83:865-8.
  7. Cazoral E, Ruiz F, Abad A, Monleon J. Prune-belly syndrome: early antenatal diagnosis. Eur J Obstet Gynecol 1997; 72:31-3.
  8. Stephens FD, Gupta D. Pathogenesis of the prune-belly syndrome. J Urol 1994; 152:2328-31.
  9. Greskovich FJ, Nyberg LM. The Prune-Belly sendrome: a review of its etiology defects, treatment and prognosis. J Urol 1988; 140:707-10.
  10. Reinberg Y, Shapiro E, Manivel JC, et al. Prune-Belly syndrome in females: A triad of abdominal musculature deficiency and anomalies of the urinary and genital systems. J Pediatr. 1991; 118:395-9.
  11. Crompton CH, Maslusky IB, Geary DF. Respiratory Function in the Prune-Belly syndrome. Arch Dis Child 1993; 68:505-6.
  12. Loder RT, Guiboux JP, Bloom DA, Hensinger RH. Musculoskeletal aspects of Prune-Belly syndrome. Description and pathogenesis. Am J Dis Child 1992; 146:1224-9.
  13. Green Ne, Lowery ER. Thomas R. Orthpaedic aspects of Prune-Belly syndrome. J Diaplatr Orthop 1993; 13:496-501.
  14. Shigeta M, Nagata M, Shimoyamada H, et al. Prune-belly syndrome diagnosed at 14 weeks' gestation with but normal kidneys. Pediatr Nephrol 1999; 13:135-7.
  15. MacMahon RA, Renou PM, Shekleton PA, Paterson PJ. Severe urethral obstruction diagnosed at 14 weeks' gestation: variability of outcome with and without drainage. Fetal Diagn Ther 1995; 10:343-8.
  16. Woodhouse CR, Ransley PG, Innes-Williams D. Prune-Belly syndrome: report of 47 cases. Arch Dis Child 1982; 52:8