Journals / Medical Network Klinik Bilimler ve Doktor / 2001 / Cilt: 7 - Sayı: 6

Pregnancy with marfan syndrome: A case report

Gebelikte marfan sendromu: Olgu sunumu

Pages
852–853
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this patient, in spite of minimal cardiovascular involvement, preeclampsia complicated pregnancy.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Marfan syndrome is a connective tissue disorder with characteristic findings in the skeletal, ocular and cardiovascular systems.
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Key Findings & Data:Maternal morbidity and mortality increase in patients with an aortic root diameter exceeding 40 mm.
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Conclusion & Impact:In this patient, in spite of minimal cardiovascular involvement, preeclampsia complicated pregnancy.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Sezaryen · Marfan sendromu · Gebelik

Abstract

Marfan syndrome is a connective tissue disorder with characteristic findings in the skeletal, ocular and cardiovascular systems. Maternal morbidity and mortality increase in patients with an aortic root diameter exceeding 40 mm. Prognosis of a patient with only minimal cardiovascular involvement will be good. We presented a 23 year-old woman with Marfan syndrome in the 36 week of her pregnancy. In this patient, in spite of minimal cardiovascular involvement, preeclampsia complicated pregnancy.

Özet

Marfan sendromu, kardiovasküler, pulmoner, oküler ve kas-iskelet sistemi tutulumu ile karakterize bir bağ dokusu hastalığıdır. Aortik kök dilatasyonu 40 mm'in üzerinde olan hastalarda maternal morbidite ve mortalite artmaktadır. Minimal kardiyovasküler tutulumu olan hastalarda prognoz iyi olacaktır. Bu yazıda 23 yaşında, 36 haftalık gebeliği olan, Marfan sendromlu ve minimal kardiyovasküler tutuluma karşın preeklampsi ile komplike olmuş bir olgu sunuldu

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Cite This Article

ÜSTÜN, Y., ÖZMEN, B., ENGİN, Y., SÖYLEMEZ, F. (2001). Pregnancy with marfan syndrome: A case report. Medical Network Klinik Bilimler ve Doktor, Cilt: 7 - Sayı: 6, 852–853. https://ajindex.com/articles/278689

References (8)

  1. Oechslin E, Turina J, Lauper U, Weiss B, Vogt P, Luscher T, Jenni R. Cardiovascular disease in pregnancy TherUmsch 1999; 56:551-60.
  2. Paternoster DM, Santarossa C, Venttore N, Dalla Pria S, Grella P. Obstetric complications in Marfan's syndrome pregnancy. Minerva Ginecol 1998; 50:441-3.
  3. Felblinger DM, Akers MC. Marfan's syndrome in pregnancy: implications for advanced practice nurses. AACN Clin Issuesl998; 9:563-8.
  4. Colman JM, Sermer M, Seaward PG, Siu SC. Congenital heart disease in pregnancy. Cardiol Rev 2000; 8:166-73.
  5. Paternoster DM, De Fusco D, Santarossa C, Lauretti E. Congenital heart disease in pregnancy. Minerva Ginecol 1999; 51:299-302.
  6. Akashi H, Tayama K, Fujino T, Onitsuka S, Sakashita H. Surgical treatment for acute type aortic dissection in pregnancy: a case of aortic root replacement just after cesarean section. Jpn Circ J 2000; 64:729-30.
  7. Rasmussen LA, Lund JT, Pettersson G. Marfan syndrome and pregnancy. Ugeskr Laeger 1998; 160:6219-20.
  8. Kudlicki J, Drozd J, Oleszczuk J. Pregnancy in women with Marfan's syndrome. Ginekol Pol 1997; 68:94-101.