Büyük pelvik nörofibroma rağmen başarılı vajinal doğum

If not otherwise fetally or maternally indicated, initiation of labor and the course of labor should be observed and vaginal delivery should be attempted for the pregnant has a pelvic neurofibroma, before a decision for cesarean section is made.

📌 3 Key Takeaways

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Objective & Hypothesis:Neurofibromatosis (NF) is an autosomal dominant genetic disorder and pregnancy in a patient with NF is associated with very poor perinatal outcome and life-threatening complications.

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Key Findings & Data:We presented a case with a large pelvic nerve tumor not causing any dystocia or obstruction to the labor, allowing vaginal delivery A 26 year old primigravida, diagnosed NF, had a large neurofibroma (about 8x9 cm diameter size) in pelvis infront of the sacrum.

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Conclusion & Impact:If not otherwise fetally or maternally indicated, initiation of labor and the course of labor should be observed and vaginal delivery should be attempted for the pregnant has a pelvic neurofibroma, before a decision for cesarean section is made.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Domain Parameters

Abstract

Neurofibromatosis (NF) is an autosomal dominant genetic disorder and pregnancy in a patient with NF is associated with very poor perinatal outcome and life-threatening complications. In addition, the growth of pelvic tumors during pregnancy can be caused to dystocia and delivery is accomplished by cesarean section. We presented a case with a large pelvic nerve tumor not causing any dystocia or obstruction to the labor, allowing vaginal delivery A 26 year old primigravida, diagnosed NF, had a large neurofibroma (about 8x9 cm diameter size) in pelvis infront of the sacrum. No significant change was detected in NF lesions. After an uneventfully antenatal follow-up, the patient gave a birth with vaginal delivery at term, even had a pelvic mass almost equal to the size of the fetal head causing no birth dystocia. If not otherwise fetally or maternally indicated, initiation of labor and the course of labor should be observed and vaginal delivery should be attempted for the pregnant has a pelvic neurofibroma, before a decision for cesarean section is made.

Özet

Nörofibromatosis (NF) otozomal dominant geçişli bir has talıktır ve NF’li olgularda gebelik, olumsuz sonuçlar ve hayatı tehdit edici komplikasyonlarla birliktelik göstermektedir. Bununla birlikte, pelvisde bulunan tümörlerdeki büyüme distosiye, buna bağlı olarak da sezaryen ile doğuma neden olabilmektedir. Bu makalede amacımız büyük pelvik nörofibroma rağmen distosiye veya doğum eyleminin ilerlemesine engel olmadan başarılı vajinal doğum gerçekleşen bir olguyu sunmaktır. 26 yaşında, primigravid ve NF tanısı almış olan gebe olguda pelvisde sakrumun ön tarafında yaklaşık 8x9 cm çapında nörofibrom mevcut idi. Gebelik boyunca olgunun NF lezyonlarında bir değişiklik saptanmamıştı. Sorunsuz bir antenatal takip sonrasında, yaklaşık fetal başa benzer bir büyüklüğe sahip pelvik kitleye rağmen distosiye neden olmadan termde, vajinal yolla doğum gerçekleşti. Pelvik nörofibroma sahip bir gebede başka bir nedenden dolayı fetal veya maternal endikasyon olmadığı durumda sezaryen ile doğum kararı verilmeden önce, doğum eyleminin başlaması ve ilerlemesi izlenmeli ve vajinal doğum denenmelidir.

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Cite This Article

KESKİN, H. L., TURGUT, O., ERCAN, K., KABACAOĞLU, G., ÜSTÜNER, I., AVŞAR, A. F. (2010). Büyük pelvik nörofibroma rağmen başarılı vajinal doğum. GORM:Gynecology Obstetrics & Reproductive Medicine, Cilt: 16 - Sayı: 2, 123–126. https://ajindex.com/articles/227014

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