On account of fact that the restenosis rate after surgical repair is very high and its clinical course is poor, we decided to present this case.
📌 3 Key Takeaways
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Objective & Hypothesis:The association of congenital pulmonary vein stenosis and cor triatriatum with normal connection to left atrium is very rare with only a few cases reported in the literature.
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Key Findings & Data:The association of congenital pulmonary vein stenosis and cor triatriatum with normal connection to left atrium is very rare with only a few cases reported in the literature.
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Conclusion & Impact:On account of fact that the restenosis rate after surgical repair is very high and its clinical course is poor, we decided to present this case.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Anjiyografi · Kor triatriatum · Kadın
Abstract
The association of congenital pulmonary vein stenosis and cor triatriatum with normal connection to left atrium is very rare with only a few cases reported in the literature. On account of fact that the restenosis rate after surgical repair is very high and its clinical course is poor, we decided to present this case.
Özet
Sol atriyuma bağlantısı normal olan konjenital pulmoner ven stenozu ile kor triatriyatum birlikteliği son derece nadir olup, literatürde az sayıda bildirim mevcuttur. Cerrahi onarım sonrası restenoz riski çok yüksek ve klinik seyri kötü olan bu anomaliyi bir olgumuz nedeniyle tartışmak istedik.
OKUTAN, V., YOZGAT, Y., VARAN, B., TOKEL, K., MERCAN, Ş., LENK, M. K., ÖZKUTLU, S. (2006). Congenital pulmonary vein stenosis and cor triatriatum: an anomaly with a rare association. Gülhane Tıp Dergisi, Cilt: 48 - Sayı: 4, 232–235. https://ajindex.com/articles/226225
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