Left pulmonary aplasia (Agenesis)

Key Findings & Data:Associated anomalies are found in more than 50% of the patients, mainly involving the cardiovascular, gastrointestinal, musculoskeletal, ürogenital systems.

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Conclusion & Impact:We present a case of pulmonary aplasia since it is a rare clinical entity.

🔬Design:Research Article

📍Scope:Comprehensive Sample

⚙️Variables:Akciğer · Erişkin · Lung

Abstract

Unilateral pulmonary aplasia (agenesis) is a rare congenital anomaly. Associated anomalies are found in more than 50% of the patients, mainly involving the cardiovascular, gastrointestinal, musculoskeletal, ürogenital systems. It is usually diagnosed in childhood but patients who have no or mild associated anomalies may survive into adulthood. We present a case of pulmonary aplasia since it is a rare clinical entity.

Özet

Tek taraflı akciğer aplazisi (agenezi) nadir görülen konjenital bir anomalidir. Hastaların %50'den fazlasında başlıca kardiyovasküler, gastrointestinal, muskuloskelatal, ürogenital sistem olmak üzere diğer sistem anomalileri de eşlik edebilmektedir. Tanısı genellikle çocukluk çağında konur. Ancak eşlik eden anomalisi olmayan ya da hafif olan hastalar erişkin yaşa kadar yaşayabilmektedirler. Nadir görülmesi nedeniyle erişkin yaşta tanı konmuş bir pulmoner aplazi olgusunu sunmayı,uygun bulduk.

Keywords

Akciğer Erişkin Lung Adult

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Cite This Article

DENİZ, Ö., TOZKOPARAN, E., ÇİFTÇİ, F., ÖZKAN, M., BİLGİÇ, H., EKİZ, K., DEMİRCİ, N. (2004). Left pulmonary aplasia (Agenesis). Gülhane Tıp Dergisi, Cilt: 46 - Sayı: 1, 56–58. https://ajindex.com/articles/225715

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