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Journals / Ege Tıp Dergisi / 2002 / Cilt: 41 - Sayı: 4

Poems sendromu 10 yaşında kız olgu

Poems syndrome in A-10-year-old girl: A case report

Şeref TARHAN
Emre ÇEÇEN
Füsun ATLIHAN
Ceyhun DİZDARER
Ferah GENEL
Pages
251–253
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

To our knowledge, she is the youngest case of POEMS syndrome who has been reported.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:POEMS syndrome has been defined as an association of plasma cell dyscrasia with polyneuropathy, organomegaly, endocrinopathy, M protein and skin changes.
📊
Key Findings & Data:A 10-year-old girl presented with polyneoropathy, diabetes mellitus type I, double monoclonal gammopathy ( IgA and IgG ), hepatomegaly, cardiomegaly, hyperpigmentation, and hypertricosis.
💡
Conclusion & Impact:To our knowledge, she is the youngest case of POEMS syndrome who has been reported.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Çocuk · POEMS sendromu · Polinöropatiler

Abstract

POEMS syndrome has been defined as an association of plasma cell dyscrasia with polyneuropathy, organomegaly, endocrinopathy, M protein and skin changes. In this report, we describe a case of POEMS syndrome. A 10-year-old girl presented with polyneoropathy, diabetes mellitus type I, double monoclonal gammopathy ( IgA and IgG ), hepatomegaly, cardiomegaly, hyperpigmentation, and hypertricosis. To our knowledge, she is the youngest case of POEMS syndrome who has been reported.

Özet

POEMS sendromu, plazma hücre diskrazisi ile ilişkili olarak polinöropati, organomegali, endokrinopati, M protein ve deri değişikliklerinden oluşan bir sendrom olarak tanımlanmaktadır. Bu yayında, polinöropati, kardiyomegali, hepatomegali, tip 1 diabetes mellitus, çift monoklonal gammapati (IgA ve IgG), hiperpigmentasyon ve hipertrikozisi olan 10 yaşındaki bir kız olguda POEMS sendromunu tanımlanmalıdır. Bilgilerimize göre yayımlanmış olan en genç olgudur.

🔖

Cite This Article

TARHAN, Ş., ÇEÇEN, E., ATLIHAN, F., DİZDARER, C., GENEL, F. (2002). Poems sendromu 10 yaşında kız olgu. Ege Tıp Dergisi, Cilt: 41 - Sayı: 4, 251–253. https://ajindex.com/articles/223062

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