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Journals / Ege Tıp Dergisi / 2017 / Cilt: 56 - Sayı: 2

Myasthenia gravis at childhood

Çocukluk çağı miyastenia gravis

İhsan ÇAKIR
Gamze Öztürk KARABULUT
Birsen GÖKYİĞİT
Ebru Demet AYGIT
Osman Bulut OCAK
Aslı İNAL
Pages
34–35
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this study we present a JMG patient who was planned to be operated for strabismus before referring to our clinic.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Juvenile myasthenia gravis (JMG) is the most common myasthenic disorder affecting children.
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Key Findings & Data:JMG includes a group of autoimmune antibody-mediated disorders targeting neuromuscular junction proteins.
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Conclusion & Impact:In this study we present a JMG patient who was planned to be operated for strabismus before referring to our clinic.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Juvenile myasthenia gravis (JMG) is the most common myasthenic disorder affecting children. JMG includes a group of autoimmune antibody-mediated disorders targeting neuromuscular junction proteins. The clinical hallmark of the disease is fluctuating and fatigable skeletal muscle weakness, which improves with rest. Ocular symptoms could be the first signs of the disease as ptosis, ophthalmoplegia, and/or diplopia. In this study we present a JMG patient who was planned to be operated for strabismus before referring to our clinic.

Özet

Jüvenil miyastenia gravis (JMG) çocukları etkileyen en yaygın miyastenik hastalıktır. JMG nöromüsküler kavşak proteinlerini hedef alan bir grup otoimmün antikor kaynaklı hastalığı içerir. Hastalığın klinik belirtisi dinlenmekle azalan istemli kaslarda yorgunluk ve güçsüzlüktür. Ptozis, oftalmopleji ve bunlara eşlik eden diplopi hastalığın ilk belirtisi olabilmektedir. Bu yazıda, dış merkezlerde strabismus sebebiyle operasyon önerilen bir JMG olgusu sunulmaktadır.

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Cite This Article

ÇAKIR, İ., KARABULUT, G. Ö., GÖKYİĞİT, B., AYGIT, E. D., OCAK, O. B., İNAL, A. (2017). Myasthenia gravis at childhood. Ege Tıp Dergisi, Cilt: 56 - Sayı: 2, 34–35. https://ajindex.com/articles/222708

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References (10)

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