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Journals / Haseki Tıp Bülteni / 2016 / Cilt: 54 - Sayı: 2

Anesthetic Management of a Patient With JarchoLevin Syndrome

Jarcho Levin Sendromlu Olguda Anestezi Yönetimi

Gamze KÜÇÜKOSMAN
BENGÜ GÜLHAN AYDIN
Aslı YALÇIN
Hilal Peri AYOĞLU
Pages
115–117
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Due to its rarity and little information in the literature related to anesthetic practice for this syndrome, we present our anesthetic experience of inguinal hernia surgery in a patient with JLS.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Jarcho-Levin syndrome (JLS) is a rare disease involving costovertebral anomalies and is accompanied by hydrocephalus, neural tube defect, and cardiac, renal and gastrointestinal problems.
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Key Findings & Data:Due to respiratory system pathologies, there is a high mortality rate at young ages.
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Conclusion & Impact:Due to its rarity and little information in the literature related to anesthetic practice for this syndrome, we present our anesthetic experience of inguinal hernia surgery in a patient with JLS.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Jarcho-Levin syndrome (JLS) is a rare disease involving costovertebral anomalies and is accompanied by hydrocephalus, neural tube defect, and cardiac, renal and gastrointestinal problems. Due to respiratory system pathologies, there is a high mortality rate at young ages. Due to its rarity and little information in the literature related to anesthetic practice for this syndrome, we present our anesthetic experience of inguinal hernia surgery in a patient with JLS.

Özet

Jarcho Levin sendromu (JLS) kostavertabral anomalilerin ve bunlara hidrosefali, nöral tüp defekti, kardiyak, renal ve gastrointestinal problemlerin eşlik ettiği nadir görülen bir hastalıktır. Solunum sistemi patolojileri nedeniyle erken yaşta mortalite oranı yüksektir. Nadir karşılaşılması ve literatürde JLS'ye dair anestezi pratiğinin az olması nedeniyle inguinal herni ameliyatı yapılan hastadaki anestezi deneyimimiz sunulmuştur.

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Cite This Article

KÜÇÜKOSMAN, G., AYDIN, B. G., YALÇIN, A., AYOĞLU, H. P. (2016). Anesthetic Management of a Patient With JarchoLevin Syndrome. Haseki Tıp Bülteni, Cilt: 54 - Sayı: 2, 115–117. https://ajindex.com/articles/207665

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References (10)

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