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Journals / Dokuz Eylül Üniversitesi Tıp Fakültesi Dergisi / 2012 / Cilt: 26 - Sayı: 1

Anesthetic management in a patient with Kearns-Sayre syndrome

Kearns-Sayre sendromlu bir hastada anestezi yöntemi

Abdulkadir YEKTAŞ
Sıtkı Nadir ŞİNİKOĞLU
Melehat EROL
Mevlüt ÇÖMLEKÇİ
Kerem ERKALP
Pages
51–55
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Here we aimed to report our anesthetic management of a patient with Kearns- Sayre syndrome.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Kearns-Sayre syndrome is a mitochondrial dissease characterized by a triad of features including oncet in persons younger than 20 years, chronic progressive external ophtalmoplegia and pigmentary degeneration of retina.
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Key Findings & Data:Cardiac conduction defects are significant and preventable cause of mortality.
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Conclusion & Impact:Here we aimed to report our anesthetic management of a patient with Kearns- Sayre syndrome.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Anestezi · genel · Kadın

Abstract

Kearns-Sayre syndrome is a mitochondrial dissease characterized by a triad of features including oncet in persons younger than 20 years, chronic progressive external ophtalmoplegia and pigmentary degeneration of retina. In patient with Kearns-Sayre syndrome, General anesthetic management should be carefully implemented in consideration of the potantial risk of aspiration and air-way complications due to poor pharyngeal muscle control and oral secretions. Cardiac conduction defects are significant and preventable cause of mortality. Here we aimed to report our anesthetic management of a patient with Kearns- Sayre syndrome.

Özet

Kearns-Sayre sendromu; Kronik-progresif, eksternal oftalmopleji ve pigmenter retina dejenerasyonu ile karakterize, 20 yaşından önce bulgu veren, mitokondriyal bir hastalıktır. Kearns-Sayre sendromlu hastalarda; potansiyel aspirasyon riski, zayıf faringeal kas kontrolü ve oral sekresyonlara bağlı hava yolu komplikasyonları nedeniyle, genel anestezi uygulaması dikkatli bir şekilde yürütülmelidir. Kalp iletim defektleri de hastalığın sık görülen ve önlenebilen ölümcül komplikasyonlarındandır. Bu sunuda; Kearns-Sayre sendromlu bir hastaya olan anestezik yaklaşımımızı sunmayı amaçladık.

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Cite This Article

YEKTAŞ, A., ŞİNİKOĞLU, S. N., EROL, M., ÇÖMLEKÇİ, M., ERKALP, K. (2012). Anesthetic management in a patient with Kearns-Sayre syndrome. Dokuz Eylül Üniversitesi Tıp Fakültesi Dergisi, Cilt: 26 - Sayı: 1, 51–55. https://ajindex.com/articles/175321

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