Journals / Anestezi Dergisi / 2013 / Cilt: 21 - Sayı: 2

Our experience of anesthesia in a patient with congenital afibrinogenemia undergoing acute abdominal surgery

Konjenital afibrinojenemili olguda akut batın nedeniyle anestezi deneyimimiz

Pages
135–138
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this case, we want to share our anesthesia experience in a patient with congenital afibrinogenemia who has undergone acute abdominal surgery.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Congenital afibrinogenemia is a rare inherited coagulation disorder.
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Key Findings & Data:As it can be asymptomatic, its clinical manifestations vary from minimal tendency of bleeding to life-threatening bleedings or thromboembolic events.
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Conclusion & Impact:In this case, we want to share our anesthesia experience in a patient with congenital afibrinogenemia who has undergone acute abdominal surgery.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Congenital afibrinogenemia is a rare inherited coagulation disorder. As it can be asymptomatic, its clinical manifestations vary from minimal tendency of bleeding to life-threatening bleedings or thromboembolic events. In this case, we want to share our anesthesia experience in a patient with congenital afibrinogenemia who has undergone acute abdominal surgery.

Özet

Konjenital afibrinojenemi nadir görülen herediter bir koagülasyon bozukluğudur. Klinikte asemptomatik olabileceği gibi, minimal kanamaya eğilimden hayatı tehdit edecek kanamalara ya da tromboembolik olaylara sebep olarak da kendini gösterebilir. Bu olguda, konjenital afibrinojenemi hastasında akut batın nedeniyle yapılan acil operasyondaki anestezi deneyimimizi anlatmak istedik.

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Cite This Article

DÖNMEZ, N. F., KILCI, O., ÜN, C., TÜRKASLAN, D., BARUT, T., DİKMEN, B. (2013). Our experience of anesthesia in a patient with congenital afibrinogenemia undergoing acute abdominal surgery. Anestezi Dergisi, Cilt: 21 - Sayı: 2, 135–138. https://ajindex.com/articles/171780

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References (18)

  1. Acharya SS, Coughlin A, Dimichele DM. Rare Bleeding Disorder Registry: Deficiencies of factors II, V, VII, XIII
  2. fibrinogen and dysfibrinogenemia. J Thromb Haemost. 2004
  3. Mannucci PM, Duga S, Peyvandi F. Recessively inherited coagulation disorders. Blood.2004
  4. Asselta R, Duga S, Tenchini ML. The molecular basis of quantitative fibrinogen disorders. J Thromb Haemost. 2006
  5. Acharya SS, Dimichele DM. Rare inherited disorders of fibrinogen. Haemophilia. 2008
  6. Castaman G. Prophylaxis of bleeding episodes and surgical interventions in patients with rare inherited coagulation disorders. Blood Transfus. 2008
  7. Bithell TC. Hereditary coagulation disorders.In: Lee GR et al. Wintrobe’s Clinical Hematology (ninth edition), London: 1993
  8. Lak M, Keihani M, Elahi F, Peyvandi F, Mannucci PM. Bleeding and thrombosis in 55 patients with inherited afibrinogenaemia. Br J Haematol. 1999
  9. Parameswaran R, Dickinson JP, de LS, Keeling DM, Colvin BT: Spontaneous intracranial bleeding in two patients with congenital afibrinogenaemia and the role of replacement therapy. Haemophilia. 2000
  10. Henselmans JM, Meijer K, Haaxma R, Hew J, van der MJ. Recurrent spontaneous intracerebral hemorrhage in a congenitally afibrinogenemicpatient: pitfalls and therapeutic options. Stroke. 1999
  11. Menart C, Sprunck N, Duhaut P et al. Recurrent spontaneous intracerebral hematoma in patient with afibrinogenemia. Thromb Haemost. 1998
  12. Koussi A, Economou M, Athanasiou MM. Intraabdominal hemorrhage due to a ruptured corpus luteum cyst in a girl with congenital afibrinogenemia. Eur J Pediatr. 2001
  13. Tziomalos K, Vakalopoulou S, perifanis v, Garipidou V. Treatment of congenital fibrinogen deficiency: overview and recent findings. Vascular Health and Risk management. 2009
  14. Sorensen B, Bevan D: A critical evaluation of cryoprecipitate for replacement of fibrinogen. Br J Haematol. 2010
  15. Goyal SS, Bhardway DV, Shenoy UK, et al. Anaesthetic management of a child with congenital afibrinogenemia. Indian J Anaesth. 2011
  16. Rodriguez RC, Buchnar GR, Clanton MS. Prophylactic cryoprecipitate in congenital afibrinogenemia. Clin Pediatric 1988: 207
  17. Mosesson MW: Antithrombin I. Inhibition of thrombin generation in plasma by fibrin formation. Thromb Haemost. 2003
  18. De Bosch NB, Mosesson