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Journals / art / 2017 / Cilt: 32 - Sayı: 2

Erdheim-Chester Disease With Renal Involvement: A Case Report

Ali Kürşat GANİYUSUFOĞLU
Gökşen GÖKŞENOĞLU
Burçin TUNÇ
Nurdan PAKER
Journal
art
Pages
167–170
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Erdheim-Chester disease diagnosis was confirmed with CD68(+) CD1a(-) histiocytes detected by immunohistochemical analysis of the nephrectomy specimen

📌 3 Key Takeaways

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Objective & Hypothesis:Erdheim-Chester disease is a type of non-Langerhans cell histiocytosis.
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Key Findings & Data:In this article, we present a 51-year-old male patient with skeletal and urinary system manifestations who finally underwent right nephrectomy due to renal insufficiency.
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Conclusion & Impact:Erdheim-Chester disease diagnosis was confirmed with CD68(+) CD1a(-) histiocytes detected by immunohistochemical analysis of the nephrectomy specimen
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Erdheim-Chester disease is a type of non-Langerhans cell histiocytosis. It is a rare, multisystem disorder with unknown etiology. Heterogeneity of the clinical symptoms makes the diagnosis challenging. On the other hand, knowing the signs and radiological findings of the disease helps to establish a correct diagnosis. In this article, we present a 51-year-old male patient with skeletal and urinary system manifestations who finally underwent right nephrectomy due to renal insufficiency. The diagnosis was suspected by the retroperitoneal infiltrative process and radiological findings of the tubular bones. Erdheim-Chester disease diagnosis was confirmed with CD68(+) CD1a(-) histiocytes detected by immunohistochemical analysis of the nephrectomy specimen

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Cite This Article

GANİYUSUFOĞLU, A. K., GÖKŞENOĞLU, G., TUNÇ, B., PAKER, N. (2017). Erdheim-Chester Disease With Renal Involvement: A Case Report. art, Cilt: 32 - Sayı: 2, 167–170. https://ajindex.com/articles/166114

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References (10)

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