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Journals / Causapedia / 2017 / Cilt: 6 - Sayı: 2

Conus Medullaris Myelitis Related to Sjögren’s Syndrome Mimicking Cauda Equina Syndrome: A Rare Case

Kauda Ekuina Sendromunu Taklit Eden Sjögren Sendromu ile İlişkili Konus Medullaris Miyeliti: Nadir Bir Vaka

Aslıhan AKŞAR
Murathan BERBER
SEZGİN KEHAYA
Meliha AKPINAR
BABÜRHAN FEYZULLAH GÜLDİKEN
Journal
Causapedia
Pages
155–159
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

This case wasconsidered worthy to share due to rare etiological,clinical and radiological findings

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Transversecharacterized by motor, sensory and autonomicdysfunction due to inflammation of the spinal cord.Thoracic and cervical segments of the spinal cord arefrequently involved but lumbosacral involvement isuncommon.
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Key Findings & Data:Lumbar pain, saddle-type anesthesia,paraparesis in the lower extremity and sphincterdeficit may occur in conus medullaris involvementwhich can be confused with cauda equina syndrome.Etiology includes multifocal diseases such as multiplesclerosis, multisystemic diseases such as systemiclupus erythematosus, post-infectious, post-vaccinationor idiopathic causes.
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Conclusion & Impact:This case wasconsidered worthy to share due to rare etiological,clinical and radiological findings
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Transversecharacterized by motor, sensory and autonomicdysfunction due to inflammation of the spinal cord.Thoracic and cervical segments of the spinal cord arefrequently involved but lumbosacral involvement isuncommon. Lumbar pain, saddle-type anesthesia,paraparesis in the lower extremity and sphincterdeficit may occur in conus medullaris involvementwhich can be confused with cauda equina syndrome.Etiology includes multifocal diseases such as multiplesclerosis, multisystemic diseases such as systemiclupus erythematosus, post-infectious, post-vaccinationor idiopathic causes. We report a case of acutetransverse myelitis on the conus medullaris due toSjögren's syndrome, presenting with sudden onset ofcauda equina symptoms. This involvement of myelitisdue to Sjögren's syndrome is quite rare. This case wasconsidered worthy to share due to rare etiological,clinical and radiological findings

Özet

Transvers miyelit, spinal kordun inflamasyonu sonucugelişen motor, duyusal ve otonomik disfonksiyonlakarakterize klinik bir sendromdur. Spinal kordun torakalve servikal segmentleri sık tutulurken, lumbosakraltutulum seyrektir. Konus medullaris tutulumunda kaudaekuina sendromu ile karışabilecek bel ağrısı, eyertarzında duyu kaybı, alt ekstremitede paraparezi vesfinkter kusuru ile ortaya çıkabilir. Etiyolojisinde,multipl skleroz gibi multifokal, sistemik lupuseritematozuspostinfeksiyöz, aşı yapılması sonrası ya da idiyopatiknedenler yer alır. Olgumuzda, ani başlangıçlı kaudaekuina sendromu semptomları ile prezente olup Sjögrensendromu ile ilişkili akut transvers miyelit tanısı alan birhasta sunulmaktadır. Konus medullaris bölgesini içinealan longitudinal bir tutulum, Sjögren sendromuna bağlımiyelitte oldukça nadirdir. Bu vaka, kauda ekuinasendromunu düşündüren klinik bulguları ve nadirradyolojik bulguları nedeniyle sunulmaya değergörülmüştür

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Cite This Article

AKŞAR, A., BERBER, M., KEHAYA, S., AKPINAR, M., GÜLDİKEN, B. F. (2017). Conus Medullaris Myelitis Related to Sjögren’s Syndrome Mimicking Cauda Equina Syndrome: A Rare Case. Causapedia, Cilt: 6 - Sayı: 2, 155–159. https://ajindex.com/articles/165835

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