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Journals / Acıbadem Üniversitesi Sağlık Bilimleri Dergisi / 2016 / Sayı: 4

Anesthetic Management of a Pediatric Patient With Larsen Syndrome

Larsen Sendromlu Pediatrik Hastada Anestezi Yönetimi

Mahmut Alp KARAHAN
Nuray ALTAY
Hasan Hüsnü YÜCE
Mehmet EROĞLU
Pages
230–233
Publication Date
2016-12-01
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this case report we discussed, in light of literature, the anesthetic management of a pediatric patient with Larsen syndrome who underwent a pes equinovarus surgery

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Larsen syndrome is a rare, inherited, connective tissue disorder which is characterized by facial dysmorphisms, congenital joint dislocations and multi-system involvement including musculoskeletal, respiratory, cardiovascular, and neurological systems.
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Key Findings & Data:Children with Larsen syndrome are prone to undergo a wide variety of surgical treatments for their orthopedic abnormalities.
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Conclusion & Impact:In this case report we discussed, in light of literature, the anesthetic management of a pediatric patient with Larsen syndrome who underwent a pes equinovarus surgery
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:larsen syndrome · general anesthesia · child

Abstract

Larsen syndrome is a rare, inherited, connective tissue disorder which is characterized by facial dysmorphisms, congenital joint dislocations and multi-system involvement including musculoskeletal, respiratory, cardiovascular, and neurological systems. Children with Larsen syndrome are prone to undergo a wide variety of surgical treatments for their orthopedic abnormalities. For this reason these patients may require repeated anesthetic care during surgical procedures. The major concerns about these patients regarding anesthesia include perioperative respiratory dysfunction, cardiovascular problems and difficult airway management. Laryngomalacia, tracheomalacia, bronchomalacia and subglottic stenosis are the main causes for difficult airway management in this syndrome. In this case report we discussed, in light of literature, the anesthetic management of a pediatric patient with Larsen syndrome who underwent a pes equinovarus surgery

Özet

Larsen sendromu; yüz dismorfizmi, konjenital eklem dislokasyonları ve kas-iskelet, solunum, kardiyovasküler ve nörolojik sistemleri içeren çoklu sistem tutulumu ile karakterize nadir bir kalıtsal bağ dokusu hastalığıdır. Ortopedik sorunlara bağlı olarak özellikle pediatrik hastalarda, var olan anomalileri nedeniyle, çeşitli cerrahi prosedürler geçirmek zorunda kalırlar. Bu nedenle bu hastalarda tekrarlayan anestezi ihtiyacı gerekebilmektedir. Anestezi yönetimi açısından hastaların majör problemleri genellikle perioperatif solunum fonksiyon bozuklukları, kardiyovasküler problemler ve zor havayolunu içerir. Laringomalazi, trakeomalazi, bronkomalazi ve subglottik stenoz, bu sendromun zor havayolu yönetimi açısından en büyük sorunları arasında yer alırlar. Bu olgu sunumunda Pes ekinovarus cerrahisi planlanan Larsen sendromlu çocuk hastada anestezi yönetimini literatür eşliğinde tartıştık

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Cite This Article

KARAHAN, M. A., ALTAY, N., YÜCE, H. H., EROĞLU, M. (2016). Anesthetic Management of a Pediatric Patient With Larsen Syndrome. Acıbadem Üniversitesi Sağlık Bilimleri Dergisi, Sayı: 4, 230–233. https://ajindex.com/articles/163032

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