Journals / Acıbadem Üniversitesi Sağlık Bilimleri Dergisi / 2018 / Sayı: 4

A Rare Case In Childhood: Left Atrial Rhabdomyosarcoma

Çocukluk Çağında Nadir Görülen Bir Olgu: Sol Atriyal Rabdomyosarkom

Pages
462–464
Publication Date
2018-12-01
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Emergency surgery was performed to the patient, left atrial mass was removed and the definitive diagnosis was confirmed by histopathological examination

📌 3 Key Takeaways

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Objective & Hypothesis:Primary cardiac tumors are very rare with malignant tumors generating approximately 20% of rhabdomyosarcomas.
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Key Findings & Data:Due to high mortality rates of rhabdomyosarcomas, surgical excision is required for initiating the definitive diagnosis, the relief of acute symptoms and prolongation of survival time.
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Conclusion & Impact:Emergency surgery was performed to the patient, left atrial mass was removed and the definitive diagnosis was confirmed by histopathological examination
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Rhabdomyosarcoma · atrial mass · childhood

Abstract

Primary cardiac tumors are very rare with malignant tumors generating approximately 20% of rhabdomyosarcomas. Symptoms change according to the localization of the mass. It is often diagnosed with transthoracic echocardiography or transeosophageal echocardiography. Due to high mortality rates of rhabdomyosarcomas, surgical excision is required for initiating the definitive diagnosis, the relief of acute symptoms and prolongation of survival time. Our patient was admitted with respiratory distress and pericardial effusion, and a mass was detected in the left atrium by echocardiography. Emergency surgery was performed to the patient, left atrial mass was removed and the definitive diagnosis was confirmed by histopathological examination

Özet

Primer kardiyak tümörler çok nadirdir, kalbin primer kötü huylu tümörlerinin yaklaşık %20’sini rabdomyosarkomlar oluşturur. Kitlenin lokalizasyonuna göre semptomlar değişir. Teşhis sıklıkla transtorasik ekokardiyografi veya transözefagial ekokardiyografi ile konur. Rabdomyosarkomların mortalitesi çok yüksek olduğundan, kesin teşhisin konulabilmesi, akut semptomların giderilebilmesi ve hayatta kalım süresinin uzatılabilmesi için cerrahi olarak çıkarılması öngörülmektedir. Solunum sıkıntısı ve plevral efüzyon ile gelen ve yapılan ekokardiyografide sol atriyal kitle saptanan olgu acil olarak açık kalp ameliyatına alındı, sol atriyal kitle çıkarıldı ve kesin teşhis histopatolojik inceleme sonucu konulabildi

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Cite This Article

ŞAHİN, D. A., BAŞPINAR, O., GÖKASLAN, G., KERVANCIOĞLU, M. (2018). A Rare Case In Childhood: Left Atrial Rhabdomyosarcoma. Acıbadem Üniversitesi Sağlık Bilimleri Dergisi, Sayı: 4, 462–464. https://ajindex.com/articles/162853

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References (6)

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