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Journals / Dokuz Eylül Üniversitesi Tıp Fakültesi Dergisi / 2018 / Cilt: 32 - Sayı: 2

A CASE OF RESTRICTIVE CARDIOMYOPATHY IN CHILDHOOD PRESENTING WITH WEAKNESS AND ANOREXIA

Halsizlik ve iştahsızlık yakınması ile gelen restriktif kardiyomiyopatili bir olgu

Tülay DEMİRCAN
Özgür KIZILCA
Cüneyt ZİHNİ
Bahattin ÖNCÜ
MUSTAFA KIR
Nurettin ÜNAL
Pages
151–155
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this article a patient at 2.5 years of age with RCM is discussed regarding the literature.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Restrictive cardiyomyopathy (RCM) is a very rarely diagnosed cardiyomyopathy in childhood.
📊
Key Findings & Data:Biatrial enlargement and normal sized ventricles with normal or increased ventricular wall thickness are the characteristic morphological features of RCM.
💡
Conclusion & Impact:In this article a patient at 2.5 years of age with RCM is discussed regarding the literature.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Restriktif kardiyomiyopati · Konstriktif perikardit · çocuk

Abstract

Restrictive cardiyomyopathy (RCM) is a very rarely diagnosed cardiyomyopathy in childhood. Most RCM in childhood is idiopathic with a high mortality. Biatrial enlargement and normal sized ventricles with normal or increased ventricular wall thickness are the characteristic morphological features of RCM. The differential diagnosis of constrictive pericarditis is important. In this article a patient at 2.5 years of age with RCM is discussed regarding the literature.

Özet

Restriktif kardiyomiyopati (RKMP) çocukluk çağının nadir görülen kardiyomiyopatilerindendir. Çocukluk çağı RKMP’lerinin çoğunda altta yatan patoloji bulunamaz ve mortalitesi yüksektir. Karakteristik morfolojik özelliği ventrikül boyutları normal, ventriküler duvar kalınlığı normal veya artmış ve biatriyal büyümedir. Konstriktif perikarditle ayırıcı tanısı önem taşır. Bu yazıda, 2,5 yaşında RKMP’li bir olgu literatür eşliğinde tartışılmıştır.

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Cite This Article

DEMİRCAN, T., KIZILCA, Ö., ZİHNİ, C., ÖNCÜ, B., KIR, M., ÜNAL, N. (2018). A CASE OF RESTRICTIVE CARDIOMYOPATHY IN CHILDHOOD PRESENTING WITH WEAKNESS AND ANOREXIA. Dokuz Eylül Üniversitesi Tıp Fakültesi Dergisi, Cilt: 32 - Sayı: 2, 151–155. https://ajindex.com/articles/152549

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References (8)

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