Journals / Acta Orthopaedica et Traumatologica Turcica / 2019 / Cilt: 53 - Sayı: 6

Unusual localization and aggressive progression of large infantile fibrosarcoma

Pages
507–511
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

This case suggests that these tumors may exhibit unpredictable clinical behavior

📌 3 Key Takeaways

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Objective & Hypothesis:Infantile fibrosarcoma is a very rare soft tissue tumor in infants and children most commonly located in extremities.
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Key Findings & Data:It constitutes less then 1 percent of all childhood cancers.
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Conclusion & Impact:This case suggests that these tumors may exhibit unpredictable clinical behavior
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Özet

Infantile fibrosarcoma is a very rare soft tissue tumor in infants and children most commonly located in extremities. It constitutes less then 1 percent of all childhood cancers. Prognosis and clinical course of it is relatively good compared to adult forms. Local recurrence is common but metastasis is infrequent. In this case report we present infantile fibrosarcoma with relapse and lung metastasis despite neoadjuvant chemotherapy, pelvic reconstruction surgery with wide surgical excision and adjuvant chemotherapy protocol. The patient was a 2-year-old girl at the time of diagnosis, and there was a huge mass in pelvic region. After neoadjuvant chemotherapy, type 1 pelvic resection and pelvic reconstruction with bone cement performed. The patient presented with relapse and lung metastasis 6 months after the surgery. This is the first report of pelvic infantile fibrosarcoma with pelvic resection surgery. This case suggests that these tumors may exhibit unpredictable clinical behavior

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Cite This Article

ATALAY, İ. B., TOĞRAL, G. (2019). Unusual localization and aggressive progression of large infantile fibrosarcoma. Acta Orthopaedica et Traumatologica Turcica, Cilt: 53 - Sayı: 6, 507–511. https://ajindex.com/articles/147390

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