Journals / Türk Pediatri Arşivi / 2026 / Cilt: 46 Sayı: 1

Congenital self healing reticulohistiocytosis Hashimoto Pritzker Disease : case report

Kendiliğinden düzelen doğumsal retikülohistiyositoz Hashimoto Pritzker Hastalığı : olgu sunumu

Pages
87–89
Publication Date
2011-03-01
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

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📌 3 Key Takeaways

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Objective & Hypothesis:@font face { font family: Times ; }p MsoNormal li MsoNormal div MsoNormal { margin: 0cm 0cm 0 0001pt; font size: 12pt; font family: Times New Roman ; }div Section1 { page: Section1; }
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🔬Design:Araştırma Makalesi
📍Scope:Comprehensive Sample
⚙️Variables:Histiyositoz · taşikardi · yenidoğan

Abstract

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Özet

Langerhans hücreli histiyositozlar aktive olmufl langerhans hücrelerinin klonal ço¤almas› ile belirgindir. Cilde s›n›rl› olabildi¤i gibi (do¤ufltan kendili¤inden düzelen retikülohistiyositoz: DKDR), organ tutulumu ile birlikte de olabilir. Do¤ufltan kendili¤inden düzelen retikülohistiyositoz tan›s› için cilt d›fl› tutulumun olmamas› ve lezyonlar›n kendili¤inden gerilemesi flartt›r. Uzun dönem izlemde cilt, mukoza, kemik ve hipofizi tutan tekrarlar bildirilmifltir. ‹zleminde atriyoventriküler ritim uyumsuzlu¤una ba¤l› taflikardi ata¤› geliflen bir do¤ufltan kendili¤inden düzelen retikülohistiyositoz olmas› nedeni ile sunulmufltur.

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Cite This Article

Gökmen, Z., Özkiraz, S., Kıyıcı, H., Ecevit, A., Tarcan, A. (2011). Congenital self healing reticulohistiocytosis Hashimoto Pritzker Disease : case report. Türk Pediatri Arşivi, Cilt: 46 Sayı: 1, 87–89. https://doi.org/10.4274/tpa.46.16

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