Acute poststreptococcal glomerulonephritis APSGN is one of the most common causes of hematuria in childhood nbsp; The hematological changes are not typical in APSGN except anemia due to hemodilution and mild hemolysis The concurrent occurence of idiopathic nbsp;thrombocytopenic purpura ITP and APSGN has very rarely been reported In this article due to its rarity we report a 13 year old boy with APSGN who simultaneously developed ITP Turk Arch Ped 2011; 46: 171 3
📌 3 Key Takeaways
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Objective & Hypothesis:Acute poststreptococcal glomerulonephritis APSGN is one of the most common causes of hematuria in childhood nbsp; The hematological changes are not typical in APSGN except anemia due to hemodilution and mild hemolysis The concurrent occurence of idiopathic nbsp;thrombocytopenic purpura ITP and APSGN has very rarely been reported In this article due to its rarity we report a 13 year old boy with APSGN who simultaneously developed ITP Turk Arch Ped 2011; 46: 171 3
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Key Findings & Data:Acute poststreptococcal glomerulonephritis APSGN is one of the most common causes of hematuria in childhood nbsp; The hematological changes are not typical in APSGN except anemia due to hemodilution and mild hemolysis The concurrent occurence of idiopathic nbsp;thrombocytopenic purpura ITP and APSGN has very rarely been reported In this article due to its rarity we report a 13 year old boy with APSGN who simultaneously developed ITP Turk Arch Ped 2011; 46: 171 3
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Conclusion & Impact:Acute poststreptococcal glomerulonephritis APSGN is one of the most common causes of hematuria in childhood nbsp; The hematological changes are not typical in APSGN except anemia due to hemodilution and mild hemolysis The concurrent occurence of idiopathic nbsp;thrombocytopenic purpura ITP and APSGN has very rarely been reported In this article due to its rarity we report a 13 year old boy with APSGN who simultaneously developed ITP Turk Arch Ped 2011; 46: 171 3
Acute poststreptococcal glomerulonephritis APSGN is one of the most common causes of hematuria in childhood nbsp; The hematological changes are not typical in APSGN except anemia due to hemodilution and mild hemolysis The concurrent occurence of idiopathic nbsp;thrombocytopenic purpura ITP and APSGN has very rarely been reported In this article due to its rarity we report a 13 year old boy with APSGN who simultaneously developed ITP Turk Arch Ped 2011; 46: 171 3
Özet
Çoğu olgunun ilk yaşta kaybedildiği Edward rsquo;s sendromunda 130 rsquo;dan fazla yapısal bozukluğun görüldüğü bildirilmiştir Sıkça rastlanan bozukluklar ön planda olmadığında tanı daha geç konduğundan nadir görülen bulgular da önem taşımaktadır Edward rsquo;s sendromunda şimdiye kadar özofagus atrezisi ve oksipital meningosel birlikteliği tanımlanmamış olduğundan 1400 gram ağırlığındaki kız hasta sunulmuştur.
Gülaşı, S., Turhan, A. H., Çelik, Y., Akbaş, E., Atıcı, A. (2011). A case of Edward’s syndrome with esophageal atresia and meningocele. Türk Pediatri Arşivi, Cilt: 46 Sayı: 2, 174–176. https://doi.org/10.4274/tpa.46.68
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Steffensen TS, Opitz JM, Gilbert-Barness E. Congenital perineal hernia in a fetus with trisomy 18. Fetal Pediatr Pathol; 28: 95-9. Bick D, Markowitz RI, Horwich A. Trisomy 18 associated with ectopia cordis and occipital meningocele. Am J Med Genet; 30: 805-10. Scorta A, Franceschini P, Pilotti G. [On a case of trisomy 18 with spina bifida and meningocele]. Minerva Ginecol 1966;: 31-6.
Edward’s sendromu/Edward’s syndrome Resim 5. Hastamıza ait 47,XX+18 bozukluğu gösteren karyotip örneği
Baty BJ, Blackburn BL, Carey JC. Natural history of trisomy 18 and trisomy 13: I. Growth, physical assessment, medical histories, survival and recurrence risk. Am J Med Genet 1994;: 175-88.
Suranyi A, Bito T, Vojda G, et al. Unusual clinical history of a male infant with Edward’s syndrome. Pathol Oncol Res 2009;: 147-52.
Steffensen TS, Opitz JM, Gilbert-Barness E. Congenital perineal hernia in a fetus with trisomy 18. Fetal Pediatr Pathol; 28: 95-9. Bick D, Markowitz RI, Horwich A. Trisomy 18 associated with ectopia cordis and occipital meningocele. Am J Med Genet; 30: 805-10. Scorta A, Franceschini P, Pilotti G. [On a case of trisomy 18 with spina bifida and meningocele]. Minerva Ginecol 1966;: 31-6.