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Journals / Causapedia / 2019 / Cilt: 8 - Sayı: 2

Nutritional Disorder in a 22-Month-Old Child due to a Rare Pathology: Plexiform Neurofibroma on the Lower Lip Kulak, Burun, Boğaz Hastalıkları

Yirmi İki Aylık Bir Çocukta Beslenme Bozukluğu Oluşturan Nadir Bir Patoloji: Alt Dudakta Pleksiform Nörofibroma

İbrahim HİRA
Mustafa ŞAHİN
ALİ TURAN BAYRAM
Mehmet YAŞAR
Fatma ÇEVİK KAYA
Journal
Causapedia
Pages
67–70
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

This case is presented due to its rarity and unusual clinical complaints.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Plexiform neurofibromas are benign tumors that originate from peripheral nerve cells.
📊
Key Findings & Data:Plexiform neurofibroma can be single or multiple as a component of neurofibromatosis type 1.
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Conclusion & Impact:This case is presented due to its rarity and unusual clinical complaints.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Abstract

Plexiform neurofibromas are benign tumors that originate from peripheral nerve cells. Although, they are generally asymptomatic, they may cause symptoms related to nerve-induced pain, paresis, or mass effect. Plexiform neurofibroma can be single or multiple as a component of neurofibromatosis type 1. In this study, we presented a plexiform neurofibroma case that caused nutritional disorder in a 22-month-old boy with neurofibromatosis type 1. Total surgical excision was performed. During the postoperative follow-up, the patient's nutrition improved and no recurrence was observed in the 18-month follow-up. This case is presented due to its rarity and unusual clinical complaints.

Özet

Pleksiform nörofibromalar periferik sinir hücrelerinden kaynaklanan benign tümörlerdir. Genellikle, asemptomatik olmalarına rağmen tuttukları sinire bağlı ağrı, parezi veya bulundukları yerde kitle etkisi nedeni ile semptomlar oluşturabilirler. Tek ya da nörofibromatozis tip 1’in bileşeni olarak multiple olabilirler. Çalışmamızda nörofibromatozis tip 1 tanısıyla takipli 22 aylık erkek hastada, beslenme bozukluğuna neden olan alt dudak yerleşimli pleksiform nörofibroma olgusu sunulmuştur. Tedavide total cerrahi eksizyon uygulanmıştır. Ameliyat sonrası izleminde hastanın beslenmesi düzeldi ve onsekiz aylık takibinde nüks izlenmedi. Bu olgu nadir görülmesi ve sıra dışı şikayeti nedeniyle sunulmuştur.

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Cite This Article

HİRA, İ., ŞAHİN, M., BAYRAM, A. T., YAŞAR, M., KAYA, F. Ç. (2019). Nutritional Disorder in a 22-Month-Old Child due to a Rare Pathology: Plexiform Neurofibroma on the Lower Lip Kulak, Burun, Boğaz Hastalıkları. Causapedia, Cilt: 8 - Sayı: 2, 67–70. https://ajindex.com/articles/143243

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References (8)

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