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Journals / Cukurova Medical Journal / 2017 / Cilt: 42 - Sayı: 3

Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency

Glukoz 6 fosfat dehidrogenaz eksikliği olan pediatrik hastada anestezi yönetimi

Sedef Gülçin URAL
Meltem Aktay İNAN
Pages
552–555
Publication Date
2017-09-30
DOI
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

In this case we aim to share applying general anesthesia safely in patients with G6PD deficiency

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Glucose 6 phospate dehydrogenase (G6PD) deficiency is the most common enzyme deficiency.
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Key Findings & Data:It is inherited in an X-linked recessive pattern and cause some disorders like hyperbilirubinemia in newborns, acut and chronic hemolysis.
💡
Conclusion & Impact:In this case we aim to share applying general anesthesia safely in patients with G6PD deficiency
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Glucose 6 phospate dehydrogenase deficiency · anesthesia management · pediatric patient.

Abstract

Glucose 6 phospate dehydrogenase (G6PD) deficiency is the most common enzyme deficiency. It is inherited in an X-linked recessive pattern and cause some disorders like hyperbilirubinemia in newborns, acut and chronic hemolysis. The first and main goal of the anethesia in this patient is to prevent oxidative stress. In this case we aim to share applying general anesthesia safely in patients with G6PD deficiency

Özet

Glukoz 6 fosfat dehidrogenaz (G6PD) enzim eksikliği en sık görülen enzim eksikliğidir. X e bağlı resesif geçişli olan bu hastalık yenidoğan hiperbilirübinemisi, akut veya kronik hemoliz gibi bir dizi bozukluklara neden olur. Bu hastalar için genel anestezinin ilk ve temel hedefi oksidatif stres gelişimini önlemektir. Bu vakayı G6PD enzim eksikliği bulunan hastalarda genel anestezinin güvenli bir şekilde uygulanabileceğini vurgulamak amacı ile paylaşmayı amaçladık.

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Cite This Article

URAL, S. G., İNAN, M. A. (2017). Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency. Cukurova Medical Journal, Cilt: 42 - Sayı: 3, 552–555. https://ajindex.com/articles/143038

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