Journals / Sakarya Tıp Dergisi / 2013 / Volume: 3 Issue: 4

Isolated Hemihypertrophy (Hemihyperplasia): A case report and review of the literature

İzole Hemihipertrofi (Hemihiperplazi): Bir olgu sunumu ve literatür derlemesi

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Publication Date
2013-12-01
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

Consequently, along with the literature, we present a case of patient with Isolated Hemihypertrophy.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Hemihypertrophy (Hemihyperplasia) is characterized by asymmetric overgrowth of cranium, face, trunk, limbs and digits.
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Key Findings & Data:In both syndromic and isolated hemihypertrophy there are an increased risk of embryonal tumors, most commonly Wilms tumor, although other abdominal tumors such as hepatoblastoma and adrenal cell carcinoma also ocur.
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Conclusion & Impact:Consequently, along with the literature, we present a case of patient with Isolated Hemihypertrophy.
🔬Design:Article
📍Scope:Comprehensive Sample
⚙️Variables:Hemihypertrophy · Hemihyperplasia · Beckwith-Wiedemann syndrome

Abstract

Hemihypertrophy (Hemihyperplasia) is characterized by asymmetric overgrowth of cranium, face, trunk, limbs and digits. It may be an isolated form or it may occur in several syndromes. In both syndromic and isolated hemihypertrophy there are an increased risk of embryonal tumors, most commonly Wilms tumor, although other abdominal tumors such as hepatoblastoma and adrenal cell carcinoma also ocur. Consequently, along with the literature, we present a case of patient with Isolated Hemihypertrophy.

Özet

Hemihipertrofi (hemihiperplazi) kranium, yüz, gövde, ekstremite ve parmakların asimetrik büyümesi ile karakterizedir. İzole olabileceği gibi bazı sendromlarda görülebilmektedir. Hem sendromik hem de izole hemihipertrofide Willms tümörü, hepatoblastom ve adrenal hücre karsinomu gibi embroyonel ve abdominal tümörlerin görülme sıklığı artmıştır. Bizde bu açıdan izole hemihipertrofili olguyu literatür eşliğinde sunuyoruz.

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Cite This Article

Yazmalar, L., Sarıyıldız, M. A., Batmaz, İ., Çavaş, H. (2013). Isolated Hemihypertrophy (Hemihyperplasia): A case report and review of the literature. Sakarya Tıp Dergisi, Volume: 3 Issue: 4. https://doi.org/10.5505/sakaryamj.2013.42714

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References (6)

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