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Journals / Eurasian Journal of Medicine and Oncology / 2019 / Cilt: 3 - Sayı: 3

Deep Sedation in Difficult Airway Patient: Case Report About Dental Treatment of Hurler Scheie Syndrome (MPS IH/IS) Patient

SEHER ORBAY YAŞLI
Dilek GÜNAY CANPOLAT
Pages
227–230
DOI
—
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

We aimed to describe our experience of deep sedation for dental treatment in a child with Hurler-Scheie syndrome.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:There are a wide range of special care patients in dentistry anesthesia.
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Key Findings & Data:As a consequence of this condition, rare syndroms are encountered.
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Conclusion & Impact:We aimed to describe our experience of deep sedation for dental treatment in a child with Hurler-Scheie syndrome.
🔬Design:Research Article
📍Scope:Comprehensive Sample
⚙️Variables:Domain Parameters

Özet

There are a wide range of special care patients in dentistry anesthesia. As a consequence of this condition, rare syndroms are encountered. Hurler-Scheie syndrome is an inherited disorder of mucopolysaccharide metabolism, which is caused by a defect in genetically controlled pathways of lysosomal degradation. As a result, mucopolysaccharide accumulation occurs in various tissues and organs. Structural and functional deficits resulting from Hurler-Scheie Syndrome can lead to difficulties in providing safe airway, especially during anesthetic applications. There is limited data on the literature about the deep sedation practice in patients with Hurler-Scheie syndrome. We aimed to describe our experience of deep sedation for dental treatment in a child with Hurler-Scheie syndrome.

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Cite This Article

YAŞLI, S. O., CANPOLAT, D. G. (2019). Deep Sedation in Difficult Airway Patient: Case Report About Dental Treatment of Hurler Scheie Syndrome (MPS IH/IS) Patient. Eurasian Journal of Medicine and Oncology, Cilt: 3 - Sayı: 3, 227–230. https://ajindex.com/articles/125939

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References (15)

  1. Noh H, Lee JI. Current and potential therapeutic strategies for mucopolysaccharidoses. J Clin Pharm Ther 2014
  2. 215–24. 2. Bjoraker KJ, Delaney K, Peters C, Krivit W, Shapiro EG. Long term outcomes of adaptive functions for children with mucopolysaccharidosis I (Hurler syndrome) treated with hematopoietic stem cell transplantation. J Dev Behav Pediatr 2006
  3. 290–96. 3. Wraith JE. The first 5 years of clinical experience with laronidase enzyme replacement therapy for mucopolysaccharidosis I. Expert Opin Pharmacother 2005
  4. 489–506. 4. Hinek A, Wilson SE. Impaired elastogenesis in Hurler disease: dermatan sulfate accumulation linked to deficiency in elastinbinding protein and elastic fiber assembly. Am J Pathol 2000
  5. 925–38. 5. Thomas S, Tandon S. Hurler syndrome: a case report. J Clin Pediatr Dent 2000
  6. 335–8. 6. Ramsay MA, Savege TM, Simpson BR. Controlled sedationwith alphaxalone-alphadolone. BMJ 1974
  7. 656–9. 7. Cortiñas-Saenz M, Martínez-Gómez L, Roncero-Goig M, SaezCuesta U, Ibarra-Martin M. Results of a major ambulatory oral surgery program using general inhalational anesthesiaon disabled patients. Med Oral Patol Oral Cir Bucal 2009
  8. e605–11. 8. Guffon N, Souillet G, MaireI Straczek J, Guibaud P. Follow up of nine patients with Hurler syndrome after bone marrow transplantation. J Pediatr 1998
  9. 119–25. 9. Kliegman RM, Behrman RE, Schor NF, St. Geme III JW and Stanton BF. Nelson Textbook of Pediatrics. 19th ed. Philadelphia: W.B. Saunders Company
  10. 480–510. 10. Herrick IA, Rhine EJ. The mucopolysaccharidoses and anaesthesia: a report of clinical experience. Can J Anaesth 1988
  11. 67–73. 11. Walker R, Belani KG, Braunlin EA, Bruce IA, Hack H, Harmatz PR, et al. Anaesthesia and airway management in mucopolysaccharidosis 2013
  12. 211–9. 12. John A, Fagondes S, Schwarts I. Sleep abnormalitiesin untreated patients with mucopolysaccharidosis type VI. Am J Med Genet A 2011
  13. 155A:1546–51. 13. Frawley G, Fuenzalide D, Donath S. A retospective audit of anaesthetic techniques and complications in children with mucopolysaccharidosis. Pediatr Anaesth 2012
  14. 737–44. 14. Fleisher LA, Beckman JA, Brown KA. ACCF/AHA focused update on perioperative beta blockade incorporated in to the ACC/AHA 2007 guidelines on perioperative cardiovasculer evaluatiın and care for noncardiac surgery: a report of the American Collage of Cardiology Foundation/American Heart Association Task Force on Practice Guidelines. Circulation 2009
  15. e169–276. 15. Bonow RO, Carabello