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Journals / Celal Bayar Üniversitesi Sağlık Bilimleri Enstitüsü Dergisi / 2026 / Volume: 8 Issue: 1

General Anesthesia Management in a Patient with Triple A Syndrome

Triple A Sendromlu Hastada Genel Anestezi Yönetimi – Olgu Sunumu

İsmet Topçu(MANİSA CELÂL BAYAR ÜNİVERSİTESİ)0000-0002-2783-2865
İlknur Bahar Başkavas(MANİSA CELÂL BAYAR ÜNİVERSİTESİ)0000-0002-6981-3857
Pages
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Publication Date
2021-03-31
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AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

With this case, we aimed to share our experiences regarding the points to be considered in an anesthesia method with triple A syndrome.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Triple A (Allgrove, AAA) syndrome is a rare autosomal recessive disorder that coexists with achalasia, alacrimia and adrenocorticotropic hormone–resistant adrenal insufficiency.
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Key Findings & Data:Neurological disorders and autonomic neuropathy are often conditions with this syndrome.
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Conclusion & Impact:With this case, we aimed to share our experiences regarding the points to be considered in an anesthesia method with triple A syndrome.
🔬Design:Case Report
📍Scope:Comprehensive Sample
⚙️Variables:Achalasia · Adrenal crisis · Alacrimia

Abstract

Triple A (Allgrove, AAA) syndrome is a rare autosomal recessive disorder that coexists with achalasia, alacrimia and adrenocorticotropic hormone–resistant adrenal insufficiency. Neurological disorders and autonomic neuropathy are often conditions with this syndrome. Adrenal insufficiency; may cause an adrenal crisis in conditions such as surgery, infection, or trauma. This can put anesthetists in difficult situations during anesthesia for various surgeries. With this case, we aimed to share our experiences regarding the points to be considered in an anesthesia method with triple A syndrome.

Özet

Triple A (Allgrove, AAA) sendromu akalazya, alakrima ve adrenal yetmezliğin birlikte görüldüğü nadir otozomal resesif bir bozukluktur. Nörolojik bozukluklar ve otonom nöropati de bu sendromla birlikte sık görülen durumlardır. Adrenal yetmezlik; ameliyat, enfeksiyon veya travma gibi durumlarda adrenal krize sebep olabilir. Bu da çeşitli ameliyatlar için anestezi sırasında anestezistleri zor durumlarla karşı karşıya getirebilir. Bu olgu ile Triple A sendromlu bir çocuğun anestezi yönteminde dikkat edilmesi gereken noktalarla ilgili deneyimlerimizi paylaşmayı amaçladık.

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Cite This Article

Topçu, İ., Başkavas, İ. B. (2021). General Anesthesia Management in a Patient with Triple A Syndrome. Celal Bayar Üniversitesi Sağlık Bilimleri Enstitüsü Dergisi, Volume: 8 Issue: 1. https://doi.org/10.34087/cbusbed.784118

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