Journals / İstanbul Tıp Fakültesi Dergisi / 2008 / Cilt: 71 - Sayı: 4

İKİ VAKA NEDENİYLE TROMBOTİK TROMBOSİTOPENİK PURPURA

Pages
124–126
Publication Date
2011-11-14
DOI
—
🏛️Bibliographic metadata and full text access for this article are provided via DergiPark.
DergiPark Record ↗
✨

AI Summary & Key Takeaways

AI Insight
⚡ TL;DR(Too Long; Didn't Read)

İki vaka nedeniyle, TTP güncel literatür ışığında tekrar gözden geçirilmiştir.

📌 3 Key Takeaways

🎯
Objective & Hypothesis:Trombotik Trombositopenik Purpura (TTP) ; Ateş, akut böbrek yetmezliği, nörolojik bozukluklar, trombositopeni ve mikroanjiopatik hemolitik anemi ile seyreden bir sendromdur.
📊
Key Findings & Data:Nadir görülen bu hastalık (4-11/1.000.000), klinik olarak dissemine intravasküler koagulasyon (DİK), hemolitik üremik sendrom (HÜS) ve Evans sendromu gibi anemi yapan diğer nedenlerle karışabilir.
💡
Conclusion & Impact:İki vaka nedeniyle, TTP güncel literatür ışığında tekrar gözden geçirilmiştir.
🔬Design:Review & Systematic Survey
📍Scope:Comprehensive Sample
⚙️Variables:Trombositopeni · Purpura · Plazmaferez

Özet

Trombotik Trombositopenik Purpura (TTP) ; Ateş, akut böbrek yetmezliği, nörolojik bozukluklar, trombositopeni ve mikroanjiopatik hemolitik anemi ile seyreden bir sendromdur. Nadir görülen bu hastalık (4-11/1.000.000), klinik olarak dissemine intravasküler koagulasyon (DİK), hemolitik üremik sendrom (HÜS) ve Evans sendromu gibi anemi yapan diğer nedenlerle karışabilir. İki vaka nedeniyle, TTP güncel literatür ışığında tekrar gözden geçirilmiştir.

🔖

Cite This Article

ERSOY, U., AKDOĞAN, M. F., PALİT, F., ŞAVLI, H., MAĞIN, H., GÜCÜN, M., ALL., A. (2011). İKİ VAKA NEDENİYLE TROMBOTİK TROMBOSİTOPENİK PURPURA. İstanbul Tıp Fakültesi Dergisi, Cilt: 71 - Sayı: 4, 124–126. https://ajindex.com/articles/104691

📄 Full Text PDF Viewer

📄

PDF görüntüleyici hazırlanıyor...

References (5)

  1. Allford SL,Hunt BJ, Rose P, Machine S. Guidelines on the diag- nosis and management of the thrombotic microangiopathic ha- emolytic anaemias. Br J Haematol 2003;120:556-573.
  2. Carmichae DS, Medley DRK.Heparin in thrombotic microan- giopathy Lancet 1966;1:1421-1424. Current concepts in thrombotic thrombocytopenic purpura. Annu Rev Med 2006; 57: 419-436).
  3. Del Zoppo, G.J.: Antiplatelet theraphy in thrombotic throm- bocytopenic purpura. Semin Hematology 1987; 24:32. Elliot MA, Nichols, WL.Thorombotic trombositopenic purpura and hemolitic uremic syndrome.Mayo Clin Proc 2001;76:1154- 1162. Feldman JD, Mardiney MR,Unanue ER,Cutting H.The vascu- lar pathology of thrombotic thrombocytopenic purpura.An im- munohistochemical and ultra structural study. Lab Invest 1966;15:927-946. GA Rock. KH Shumak. NA Buskard.VS Blanchette.JG Kel- ton.RC Nair and RA Spasoff comparison of plasma exchange with plasma infusion in the treatment of thrombotic thrombocy- topenic purpura canadian Apheresis study group N Eng J Med 1991;325:393-397. James N.George How I treat patients with thrombotic throm- bocytopenic purpura- hmolytic uremic syndrome. Blood 2000;96:1223-1229. George JN,Gilcher RO,Smith JW, Chandler L, Duvall D.Thrombotic Thrombocytopenic Purpura – Hemolytic Uremic Syndrome: diagnosis nand manangement.J Clin Apheresis 1998;13:120-125. Havens,P.L.,O’Rouke P.P.,Hahn,J.,Higgins,J., Walker,A.M.:La- boratory and clinical varables to predict outcome in hemolytic- üremic syndrome AJDC 1988;142:961. James N. George, Thorombotic trombositopenic purpura N Engl J Med 2006;354:1927-3195.
  4. Kennedy SS, Zacharsky LR,Beck JR.Thrombotic thrombosito- penic purpura:analysis of 48 unselected cases. Semin Thromb Hemost 1980;6:341-349. Kutell MA,Alfrey CP,Hetting RA.TTP treatment N Engl J Med 1971;285:971-972.
  5. Melnyk, A.M.S.,Solez K., Kjellstrand, C.M.:Hemolytic uremic syndrome in adults. Arch Intern Med 1995;155:2077. Miller,J.M., Pastorek,JG.:Thrombotic thrombocytopenic purpu- ra and hemolytic üremic syndrome in pregnancy.Clin Obstet Gynecol 1991;34:41. Neame PB.Immunologic and other factors in thrombotic throm- bocytopenic purpura (TTP). semin Thromb Hemost 1980;6:416- 429. Ponticelli,C.,Rivolta,E.,Imbasciati,E., Rossi,E., Mannuc- ci,P.M.:Hemolytic üremic syndrome. Arch Intern Med 1980; 140:335. Rock,G.A.,Shumak,K.H.,Buskard,N.A.: Comparision of plasma Exchange with plasma infusion the treatment of TTP N Eng J Med 1991;325:326. Rock G,Porta C, Bobbio-Pallavicini E.Thromboti