Three cases with Klippel-Trenaunay syndrome and treatment options

Abstract

Klippel-Trenaunay syndrome (KTS) is a rare congenital anomaly characterized by capillary malformations,soft tissue and bone hypertrophy and varicosities. The presence of at least two of the three clinical conditionsis sufficient for the diagnosis of KTS. Early diagnosis and treatment are important because of possible seriouscomplications such as deep vein thrombosis and pulmonary embolism. Venous system aplasia and/or hypoplasiamight be observed in KTS. Therefore, deep venous system must be evaluated definitely before determiningthe treatment strategy. It's herein presented our conservative and surgical treatment applications in three KTSpatients.