Peutz Jeghers sendromu

Abstract

Peutz - Jeghers Syndrome is a rare, inherited aut&zomal dominant disease characterized by gastrointestinal hamartomatous polyps and milcocutaneous pigmentation. In this paper we report two cases of Peutz -Jeghers syndrome who were admitted and operated with intussusception. Screening theirfamily members revealed intestinal and extraintestinal manifestations of the disease and no malignancy was detected.