A rare case of isolated female epispadias

Abstract

Isolated female epispadias without bladder exstrophy is an extremely rare entity. It usually presents with primary urinary incontinence and abnormal external genitalia. We describe this rare congenital anomaly in a 7-year-old girl who presented with urinary incontinence and abnormal external genitalia. She had a bifid clitoris and widely separated labia minora. The vagina was normal. Voiding Cysto-urethrography (VCUG) showed small capacity bladder with no reflux. Surgical reconstruction of the urethra, labia minora and clitoris was performed.