Juvenile psammomatoid ossifying fibroma with skull base and orbital wall invasion: a rare case report

Kafa tabanı ve orbita duvarına invazyongösteren jüvenil psammomatoid ossifiye fibrom: Ender görülen bir olgu sunumu

Özet

Jüvenil ossifiye fibrom nadir görülen, benign ancak lokal agresif bü- yüme paterni gösteren bir fibroosseöz lezyondur. Di¤er fibroosseöz tümörlerden, özellikle hastal>¤>n bafllang>ç yafl>, agresif davran>fl> ve klinik presentasyonu ile ayr>l>r. mlanm>flt>r; trabeküler ve psammomatoid varyant. Çal>flmam>zda, genç bir erkek çocukta sinonazal bölge, kafa taban> ve orbitay> tutan ve endoskopik olarak tedavi edilen bir psammomatoid ossifiye fibrom olgusunu sunduk.

Abstract

Juvenile ossifying fibroma is an uncommon, benign, fibro-osseous neoplasm with aggressive local growth. This tumor is distinguished fromother fibro-osseous lesions especially by its age of onset, aggressivebehavior, and clinical presentation. Two microscopic types have beendescribed: trabecular and psammomatoid variants. In this case report, wepresented a young male patient with juvenile psammomatoid ossifyingfibroma involving the sinonasal region, skull base and the orbit, whichwas treated with endoscopic surgery.