INFRAHYOID VAGAL PARAGANGLIOMA: REPORT OF A RARE CASE

Özet

Paragangliomas are neuroendocrine tumors which develop from extra-adrenal paraganglia tissues. This tissues derivate from neural crest and relate to autonomous nerve system. Head and neck paragangliomas are generally non-functioned unlike pheochromocytoma. The first symptom is slowgrowing mass in neck usually. A 42-year-old woman was admitted to otolaryngology clinic with the complaint of neck mass which was slow-growing. There was a 5 cm, painless, semi-mobile mass in her right neck. There was no other pathological finding. It was a 33 mm mass behind the carotis in ultrasound examiation. It was hypervascular and including cystic areas. There was a 5 cm tumor which developed from therightvagalnerveintheoperation.Vagalnervewas sacrified to remove tumor. Specimen was consistent with paraganglioma. An unusual infrahyoid vagal paraganglioma case was presented in this paper. There is only one report about such a disease before in English literature.

Abstract

Paragangliomalar adrenal dışı paraganglia dokularından gelişen nöroendokrin tümörlerdir. Bu dokular nöral kresttengelişirveotonomsinirsistemiileilişkilidir.Baş boyun paragangliomaları feokromasitomanın aksine geneldeafonksiyoneldir.İlksemptomgenellikleboyunda yavaş büyüyen kitledir. 42 yaşında kadın hasta böyle boyundagittikçbüyüyenkitleşikayetiileKBBkliniğine başvurdu. Muayenede boyun sağ tarafında 5 cm, yarı mobilağrısızkitleizlendi.Ulstrasondakarotisarkasında 33 mm, vasküler ve kistik alanlar içeren kitle izlendi. Operasyonda sağ vagal sinir kaynaklı 5 cm kitle lezyon izlendi.Vagalsinirfedaedilerekkitleçıkarıldı.Patoloji paragangioma ile uyumluydu. Hyoid altı yerleşimli bir vagal paraganlioma olgusu bu yazıda sunuldu. İngilizce literatürde, buna benzer daha önce sunulmuş 1 vaka vardır.